ABSTRACT
Angiokeratoma circumscriptum is the rarest variant of angiokeratoma. It usually affects females and it is characterized by dark-red to blue-black confluent papules or nodules on lower limbs in a segmental and unilateral distribution. We describe the clinical and histopathological findings in a patient with angiokeratoma circumscriptum and discuss the etiology, associations, diagnosis, differential diagnosis, and treatment.
Subject(s)
Angiokeratoma/diagnosis , Skin Neoplasms/diagnosis , Adult , Angiokeratoma/congenital , Angiokeratoma/pathology , Diagnosis, Differential , Female , Humans , Lower Extremity , Skin Neoplasms/congenital , Skin Neoplasms/pathologyABSTRACT
Aplasia cutis congenita (ACC) associated with fetus papyraceus is a rare subtype of aplasia cutis categorized as type V in Frieden's classification. It is characterized by stellate lesions in a symmetrical distribution over the trunk and proximal extremities. Conservative treatment is recommended, but there is not a well-defined therapeutic protocol. We report the case of a type V ACC in a preterm male newborn with lesions on the trunk and scalp successfully treated with topical 1% silver sulfadiazine and petrolatum gauze with an excellent evolution. This case associates a severe affectation of the scalp which represents a rare variant of type V ACC.
Subject(s)
Ectodermal Dysplasia , Bandages , Ectodermal Dysplasia/diagnosis , Ectodermal Dysplasia/therapy , Humans , Infant, Newborn , Male , Petrolatum , Scalp , TorsoABSTRACT
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