Infantile Fibrosarcoma of the Tongue Base.

Infantile fibrosarcoma is an uncommon soft tissue tumour in infants and children mostly located in the extremities. Its occurrence in the head and neck, particularly in the oral cavity is extremely rare. Here, we report a case of infantile fibrosarcoma of the tongue base in a 9-year-old boy and discuss the complexities in arriving at diagnosis and its management. The patient underwent wide local excision of the tumour. Histopathology was essential in confirming the diagnosis. As per search in English literature, this is the first case of infantile fibrosarcoma of the tongue base to be reported till date. Treatment of choice is wide local excision with or without chemotherapy.

Paediatric nasal dermoids: Our experience / Dermoides nasales pediátricos: nuestra experiencia

OBJECTIVES: Nasal dermoids are rare developmental anomalies seen in children. This study reports our experience in a developing country of the clinical and radiological findings as well as the management of nasal dermoids. METHODS: A retrospective analysis was performed, from 2012 to 2017, for 10 patients admitted for the treatment of nasal dermoids at a tertiary care center. The clinical presentation, preoperative imaging (CT/MRI), surgical approach, intraoperative findings, complications and recurrence were reviewed. RESULTS: Ten patients were included in this study, 6 males and 4 females, with an average age of 10.2 years at the time of presentation. Three patients presented with a mass located on the nasal dorsum, 1 had a nasoglabellar mass, 2 patients had a mass located on the nasal dorsum with visible sinus, and 4 patients presented with a sinus on the nasal dorsum, in which 1 patient had a tuft of hair. CT was performed in all the cases. It was not suggestive of intracranial extension in 9 patients, and was non-diagnostic in one patient. Both CT and MRI were performed on 2 patients, with no evidence of intracranial extension. Surgical and radiological findings were concordant in 8 patients (80%). CONCLUSION: Nasal dermoids require preoperative imaging and precise surgical planning to achieve complete removal

OBJETIVOS: Los dermoides nasales son anomalías del desarrollo poco frecuentes que se observan en niños. Este estudio informa de nuestra experiencia, en un país en desarrollo, de los hallazgos clínicos y radiológicos, así como el manejo de los dermoides nasales. MÉTODOS: Se realizó un análisis retrospectivo, desde 2012-2017, ¡¿¿para 10 pacientes ingresados ?? para el tratamiento de dermoide nasal en un instituto de nivel terciario. Se revisaron la presentación clínica, las imágenes preoperatorias (TC/RM), el abordaje quirúrgico, los hallazgos intraoperatorios, las complicaciones y la recurrencia. RESULTADOS: Se incluyeron 10 pacientes en este estudio, 6 varones y 4 mujeres, con una edad promedio de 10,2 años en el momento de la presentación. Tres pacientes presentaban una masa localizada en el dorso nasal, uno tenía una masa nasoglabellar, 2 pacientes presentaban una masa localizada en el dorso nasal con seno visible y 4 pacientes presentaban un seno en el dorso nasal, de los cuales un paciente tenía un mechón de pelo. La TC se realizó en todos los casos. No sugirió una extensión intracraneal en 9 pacientes y no fue diagnóstico en un paciente. Tanto la TC como la RM se realizaron en 2 pacientes, sin evidencia de extensión intracraneal. Los hallazgos quirúrgicos y radiológicos fueron concordantes en 8 pacientes (80%). CONCLUSIÓN: Los dermoides nasales requieren imágenes preoperatorias y una planificación quirúrgica precisa para lograr una extracción completa

Paediatric nasal dermoids: Our experience.

OBJECTIVES: Nasal dermoids are rare developmental anomalies seen in children. This study reports our experience in a developing country of the clinical and radiological findings as well as the management of nasal dermoids. METHODS: A retrospective analysis was performed, from 2012 to 2017, for 10 patients admitted for the treatment of nasal dermoids at a tertiary care center. The clinical presentation, preoperative imaging (CT/MRI), surgical approach, intraoperative findings, complications and recurrence were reviewed. RESULTS: Ten patients were included in this study, 6 males and 4 females, with an average age of 10.2 years at the time of presentation. Three patients presented with a mass located on the nasal dorsum, 1 had a nasoglabellar mass, 2 patients had a mass located on the nasal dorsum with visible sinus, and 4 patients presented with a sinus on the nasal dorsum, in which 1 patient had a tuft of hair. CT was performed in all the cases. It was not suggestive of intracranial extension in 9 patients, and was non-diagnostic in one patient. Both CT and MRI were performed on 2 patients, with no evidence of intracranial extension. Surgical and radiological findings were concordant in 8 patients (80%). CONCLUSION: Nasal dermoids require preoperative imaging and precise surgical planning to achieve complete removal.