ABSTRACT
Ivemark syndrome or right atrial isomerism is a rare syndrome of asplenia / hyposplenia with malformation of heart and abnormal arrangement of internal organs of chest and abdomen and is classified under heterotaxy disorder. We describe here the case of a 14 year old boy diagnosed with asplenia, dextrocardia with double outlet right ventricle and midline liver.
Subject(s)
Abnormalities, Multiple/diagnostic imaging , Bronchiectasis/diagnostic imaging , Dextrocardia/diagnostic imaging , Double Outlet Right Ventricle/diagnostic imaging , Heart Defects, Congenital/diagnostic imaging , Heterotaxy Syndrome/diagnosis , Liver/abnormalities , Abnormalities, Multiple/diagnosis , Adolescent , Heart Defects, Congenital/diagnosis , Heterotaxy Syndrome/physiopathology , Humans , Male , Tomography, X-Ray Computed , Transposition of Great Vessels/diagnostic imagingABSTRACT
Cranio spinal dermoid tumors are rare, benign, slow growing congenital, cystic uni or multi locular tumors, which arise from the inclusion of epithelial tissue within the neural grove during embryonic development.[1] In this case report, we present an uncommon presentation, of a case of concomitant dermoid cysts at conus medullaris and cervico medullary junction that ruptured into the central canal.
