[Familial protein C-deficiency--a clinical presentation]. / Familiaer protein C-mangel--klinisk presentasjon.

Protein C is a hepatic vitamin K-dependent protein which on activation, inhibits activated factor V and VIII and involves fibrinolytic activity. Protein C deficiency is associated with increased risk of thromboembolic complications. The article presents a family with hereditary protein C deficiency and discusses information concerning and follow-up of the family members.