ABSTRACT
An infant presented with clinical signs and symptoms suggestive of a pyloric stenosis. On abdominal ultrasound, pyloric stenosis was excluded, and other causes for proximal duodenal obstruction, such as a duodenal web or annular pancreas, were suspected. At surgery, the cause was found to be due to an anterior portal vein or preduodenal portal vein, compressing the duodenum. There were no associated findings such as midgut malrotation, duodenal web and congenital anomalies. The treatment was a diamond-shaped duodeno-duodenostomy anterior to the portal vein. The patient improved after surgery.
Subject(s)
Duodenal Obstruction/congenital , Duodenal Obstruction/surgery , Portal Vein/abnormalities , Diagnosis, Differential , Female , Humans , InfantABSTRACT
A patient presented with typical features of ankylosing spondylitis, as well as some of the biochemical abnormalities expected in this disease. In addition the patient had symptoms and signs of biventricular heart failure (dilated cardiomyopathy) with conduction defect. No valve lesions were demonstrated. A non-reducible head tilt, seldom described in ankylosing spondylitis, was also present. A short review of the possible mechanisms in the development of dilated cardiomyopathy in ankylosing spondylitis is given.
