ABSTRACT
The authors present 7 cases (4 girls and 3 boys) with a high type of imperforate anus. Combined posterior sagittal and transabdominal approach was applied. In all 7 cases the height of the malformation, determined by x-ray and ultrasonography was more than 30 mm. One stage surgical procedure, without colostomy, was applied in two of the cases. One child was treated by a two stage and the other four by a three stage operation. The operation is described and the postoperative complications and the results are discussed.
Subject(s)
Anus, Imperforate/surgery , Digestive System Surgical Procedures/methods , Anus, Imperforate/diagnostic imaging , Female , Humans , Infant, Newborn , Male , Radiography , Treatment Outcome , UltrasonographyABSTRACT
A check up of literature has been made concerning the congenital microspherocytic hemolytic anemia, reporting of some new data about the pathogenesis of the disease. One family is described with CMHA--one father and his two daughters, the two children of his first daughter and the only child of the second daughter, hence confirming the familial character of the disease. All patients have been splenectomized. After the splenectomy they are practically healthy, without hemolytic crises, supporting the statement that splenectomy is the treatment of choice in CMHA therapy.
