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Asian Cardiovasc Thorac Ann ; 23(9): 1083-6, 2015 Nov.
Article in English | MEDLINE | ID: mdl-24782568

ABSTRACT

Immunoglobulin G4-related systemic disease is a rare entity with various presenting symptoms. We report the case of a 34-year-old Chinese male who presented with immunoglobulin G4-related aortitis and the unusual symptom of hoarseness of voice. He underwent distal ascending aorta and total aortic arch replacement.


Subject(s)
Aorta, Thoracic/immunology , Aortitis/diagnosis , Autoimmune Diseases/diagnosis , Hematoma/diagnosis , Immunoglobulin G/analysis , Adult , Aorta, Thoracic/diagnostic imaging , Aorta, Thoracic/surgery , Aortitis/immunology , Aortitis/surgery , Aortography/methods , Autoimmune Diseases/complications , Autoimmune Diseases/immunology , Autoimmune Diseases/surgery , Biomarkers/analysis , Biopsy , Blood Vessel Prosthesis Implantation , Diagnosis, Differential , Hoarseness/etiology , Humans , Immunohistochemistry , Male , Predictive Value of Tests , Tomography, X-Ray Computed
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