[Extrapyramidal syndrome and hypoparathyroidism. On the identity of Fahr disease]. / Síndrome extrapiramidal e hipoparatireoidismo. Acerca da identidade da doença de Fahr.

Bilateral calcifications in the basal ganglia associated with neurological manifestations was diagnosed as Fahr disease for a long time. We present the cases of two patients with bilateral calcifications in the basal ganglia who presented hypoparathyroidism and extrapyramidal syndrome. Based on literature review we discuss the identity of Fahr disease and the relationship between calcifications in the basal ganglia and manifestations of endocrine system dysfunctions.