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Asia Pac J Clin Oncol ; 7(3): 193-6, 2011 Sep.
Article in English | MEDLINE | ID: mdl-21884431

ABSTRACT

Carcinoids of the ampulla of Vater are infrequent tumors of which a quarter of cases have been detected in patients with type I neurofibromatosis. This hereditary disease is also associated with gastrointestinal stromal tumors (GIST). However, the coincidence of these three entities together have only been formerly detected in five cases. A 53 year-old female patient, diagnosed with type I neurofibromatosis, with a malignant carcinoid of ampulla of Vater and multiple gastrointestinal stromal tumors in the duodenum and jejunum, was treated with total pancreatectomy and the excision of her intestinal tumors. Five-years on, a follow-up showed the patient to be well, and free from tumor recurrence. The coexistence of an ampullary carcinoid tumor, GIST and neurofibramatosis is very rare. Radical curative surgical resection is a good treatment option, but the optimal management of this is not yet well established.


Subject(s)
Ampulla of Vater/pathology , Gastrointestinal Stromal Tumors/pathology , Neurofibromatoses/pathology , Pancreatic Neoplasms/pathology , Ampulla of Vater/surgery , Female , Gastrointestinal Stromal Tumors/surgery , Humans , Middle Aged , Neurofibromatoses/surgery , Pancreatic Neoplasms/surgery
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