ABSTRACT
Congenital left atrial appendage aneurysm (LAAA) is a very rare condition and occurs as a result of congenital dysplasia of musculi pectinate. These patients may be asymptomatic and/or may present with dyspnea, and thromboembolic events. The most common complications are life-threatening thromboembolic events and supraventricular tachyarrhythmias. Transthoracic echocardiography plays a very important role in the diagnosis of LAAA. Herein, we present a rare case of giant congenital LAAA.
Subject(s)
Atrial Appendage/abnormalities , Echocardiography/methods , Heart Aneurysm/congenital , Atrial Appendage/diagnostic imaging , Atrial Appendage/surgery , Cardiac Surgical Procedures/methods , Diagnosis, Differential , Female , Heart Aneurysm/diagnosis , Heart Aneurysm/surgery , Humans , Infant, Newborn , Rare DiseasesABSTRACT
Congenital pulmonary venous stenosis is a rare condition leads to progressive pulmonary hypertension and heart failure. It may be isolated or associated with other cardiac malformations. The condition ranges from hypoplasia of individual pulmonary veins to constriction of the intima of the venoatrial junction. We present a case of congenital PVS involving 4 pulmonary veins combined with severe valvular and subvalvular aortic stenoses.
