ABSTRACT
A thirty-three year old woman, known to have Kearns-Sayre syndrome for eight years, had an ECG pattern of right bundle branch block and left anterior fascicular block that evolved to complete atrioventricular block, leading her to a syncopal episode. A temporary pacemaker and a permanent one were installed. The patient has been asymptomatic so far.
Subject(s)
Heart Block/complications , Kearns-Sayre Syndrome/complications , Syncope/etiology , Adult , Electrocardiography , Female , Heart Block/diagnosis , Heart Block/therapy , Humans , Kearns-Sayre Syndrome/therapy , Pacemaker, Artificial , Syncope/diagnosis , Syncope/therapySubject(s)
Methylprednisolone/therapeutic use , Myocarditis/drug therapy , Rheumatic Fever , Rheumatic Heart Disease/drug therapy , Adolescent , Adult , Antibodies, Bacterial/immunology , Female , Humans , Injections, Intravenous , Male , Methylprednisolone/administration & dosage , Myocarditis/immunology , Rheumatic Fever/immunology , Streptococcus/immunologySubject(s)
Middle Aged , Humans , Female , Echocardiography , Endomyocardial Fibrosis , Diagnosis, DifferentialABSTRACT
Oito pacientes com cardite reumatica ativa a maioria em franca insuficiencia cardiaca foram tratados com esquema de pulsoterapia (lg de metilprednisolona intravenosa). Foram acompanhados por exame clinico,eletrocardiograma, radiografia de torax, provas de atividade reumatica e ecocardiograma. A melhora da insuficiencia cardiaca ocorreu em dias. Esta forma de terapeutica tornou possivel o controle da insuficiencia cardiaca, certamente imunologica em curto periodo de tempo e sem efeitos adversos. Ela permitira, tambem, maior abrangencia em situacoes especiais de insuficiencia cardiaca auto-imune