ABSTRACT
In order to document intestinal pseudo-obstruction (IPO) as a recently recognized manifestation of systemic lupus erythematosus (SLE), we report the case or a woman with SLE who presented with IPO and we review 21 other previously reported cases from an English literature search. In 41% of the cases, IPO was the initial manifestation of their underlying lupus. The clinical and laboratory features were not significantly different from those reported in large series of patients with SLE, except for an apparent association with an urinary tract involvement (ureterohydronephrosis and interstitial cystitis). The pathogenic mechanism of this complication is not fully understood, but seems to be heterogeneous. IPO responded readily to high dose steroid therapy in all patients, but in some cases this complication evolved regardless of the underlying disease activity. A high level of awareness of this complication is needed to avoid unnecessary surgical intervention.
Subject(s)
Intestinal Pseudo-Obstruction/etiology , Lupus Erythematosus, Systemic/complications , Adolescent , Adult , Child , Diagnosis, Differential , Female , Humans , Intestinal Pseudo-Obstruction/physiopathology , Lupus Erythematosus, Systemic/diagnosis , Male , Middle AgedSubject(s)
Carcinoma, Papillary/secondary , Pleural Neoplasms/secondary , Thyroid Neoplasms/pathology , Aged , Carcinoma, Papillary/diagnosis , Carcinoma, Papillary/therapy , Humans , Male , Pleural Neoplasms/diagnosis , Pleural Neoplasms/therapy , Thoracoscopy , Thyroid Gland/pathology , Thyroid Gland/surgery , Thyroid Neoplasms/therapy , Thyroidectomy , Treatment OutcomeABSTRACT
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No disponible
Subject(s)
Adult , Aged , Male , Female , Humans , Thoracoscopy , Thyroidectomy , Thyroid Gland , HIV Infections , Treatment Outcome , Carcinoma, Papillary , Diagnosis, Differential , Facial Paralysis , Thyroid Neoplasms , Pleural NeoplasmsSubject(s)
Hepatitis C, Chronic/diagnosis , Vasculitis/diagnosis , Vasculitis/drug therapy , Aged , Antiviral Agents/therapeutic use , Biopsy, Needle , Disease Progression , Drug Therapy, Combination , Fatal Outcome , Female , Hepatitis C, Chronic/complications , Humans , Immunohistochemistry , Immunosuppressive Agents/therapeutic use , Liver Function Tests , Risk Assessment , Severity of Illness Index , Vasculitis/complicationsABSTRACT
The case of a patient with the Ehlers-Danlos syndrome who presented a picture of acute cholangitis only attributable to the presence of a large duodenal diverticulum is reported. The pathologic implications of the duodenal diverticula are described with special attention being given to their participation in the development of acute cholangitis. The digestive manifestations associated to the Ehlers-Danlos syndrome are also reviewed.
