ABSTRACT
A giant retroperitoneal desmoid (30 x 15 cm), in a 16-year old girl arising from psoas fascia is reported. Despite debulking surgery, adjuvant radiotherapy, anti-oestrogen agents and non-steroidal anti-inflammatory agents, 3 years later she died from tumour invasion of major blood vessels and bowel, leading to massive gastrointestinal bleeding.
Subject(s)
Fibromatosis, Aggressive/diagnosis , Retroperitoneal Neoplasms/diagnosis , Adolescent , Female , Fibromatosis, Aggressive/pathology , Fibromatosis, Aggressive/surgery , Humans , Retroperitoneal Neoplasms/pathology , Retroperitoneal Neoplasms/surgerySubject(s)
Adenoma/pathology , Carcinoma, Renal Cell/pathology , Kidney Neoplasms/pathology , Abdominal Pain/diagnosis , Abdominal Pain/etiology , Adenoma/diagnosis , Adult , Biopsy, Needle , Carcinoma, Renal Cell/diagnosis , Carcinoma, Renal Cell/surgery , Diagnosis, Differential , Humans , Immunohistochemistry , Kidney Neoplasms/diagnosis , Kidney Neoplasms/surgery , Male , Nephrectomy , Tomography, X-Ray Computed , Ultrasonography, DopplerABSTRACT
Leiomyoma of the urethra is a rare clinical entity. We report an unusual presentation of this tumour, which led to a diagnostic and surgical dilemma. The patient was a 16-year old female who presented with a labial mass which was palpable abdominally. Imaging methods and laparoscopy demonstrated a well defined soft tissue mass arising from the pelvis, without any obvious involvement of the urinary tract. The tumour (8 x 10 cm) was completely excised with reconstruction of the bladder and urethra. Histology confirmed a cellular leiomyoma.