ABSTRACT
Introdução: O fibroodontoma ameloblástico é uma rara neoplasia composta por epitélio odontogênico em proliferação, tecido ectomesenquimal e vários graus de tecido dentário duro formação. A idade média da incidência é de 8-12 anos e não há predileção por gênero ou local anatômico, mas é mais comumente encontrados em mandíbulas de crianças ou adolescentes. Relato de caso: A paciente do sexo feminino, 3 anos de idade, apresentava edema na região anterior da maxila, com assimetria facial. Radiograficamente, apresentava-se como uma lesão de limites indefinidos. A hipótese clínica foi de odontoma. A cirurgia de enucleação foi realizada com preservação dos germes dentários. O diagnóstico final foi de fibroodontoma ameloblástico. Sem recorrência foi observado no período de acompanhamento de 1 ano, e o dente permanente germes foram posicionados corretamente para erupção. Conclusão: Embora o fibroodontoma ameloblástico é uma lesão benigna, desenvolveu-se em idade muito precoce, com rápido crescimento e destruição do osso cortical. A enucleação cirúrgica adequada permitiu a manutenção dos dentes
Introduction: The ameloblastic fibro-odontoma is a rare mixed neoplasm composed of proliferating odontogenic epithelium, ectomesenchymal tissue, and varying degrees of dental hard tissue formation. The mean age of the incidence is from 8-12 years and there is no gender or anatomic site predilection, but it is most commonly found in children's or teenager's jaws. Case report: A 3-year-old female patient showed a swelling in anterior maxilla, with facial asymmetry. Radiographically, it presented as a mixed lesion with undefined limits. Clinical hypothesis was odontoma. Enucleating surgery was conducted with tooth germs preservation. The final diagnosis was ameloblastic fibro-odontoma. No recurrence was observed at 1-year follow-up period, and the permanent tooth germs were correctly positioned for eruption. Conclusion: Although ameloblastic fibro-odontoma is a benign lesion, it developed in a very early age, with rapid growth and destruction of cortical bone. Proper surgical enucleation allowed the teeth maintenance
Subject(s)
Humans , Child, Preschool , Child , Ameloblastoma , Odontoma , Odontogenic TumorsABSTRACT
AIM: The aim of this case report is to emphasize the importance of an early diagnosis of Gardner's syndrome through the detection of lesions appearing in the oral and maxillofacial area as well as to present two cases of the disease. BACKGROUND: Gardner's syndrome is an autosomal dominant disease characterized by gastrointestinal polyps that develop in the colon as well as in the stomach and upper intestine, along with multiple osteomas, skin, and soft tissue tumors. Cutaneous findings may include desmoid tumors, epidermoid cysts, and other benign tumors. Early diagnosis and therapy of the disease are critical because polyps have a 100% risk of undergoing malignant transformation. Craniomaxillofacial manifestations (osteoma formation, tooth impaction, diffuse opacities in the skull, mandible and maxilla, scalp tumors) usually precede polyposis. REPORT: Case 1: Gardner's syndrome was diagnosed in a 25-year-old Caucasian man who was referred by his endodontist for evaluation of an uncommon radiographic image in the mandibular molar area. Further investigation revealed a familial adenomatous polyposis (FAP) complicated by adenocarcinoma of the colon. A colectomy and an ileorectal anastomosis were performed. Case 2: A 12-year-old Caucasian girl, who is a niece of the patient described in Case 1, presented with progressive difficulty with mouth opening but no complaints of digestive problems. Radiographic examination revealed multiple radiopacities in the maxilla, mandible left temporomandibular joint, and in the left mandibular angle. Multiple impacted teeth were present. A colonoscopy was suggested, but the patient's parents decided to continue the investigation and treatment with their own physician in their home town. SUMMARY: Since an early diagnosis is essential and general dental practitioners may be the first healthcare professionals to suspect the diagnosis, it is important for them to be familiar with the features of Gardner's syndrome.
