Planificación digital en tratamiento de fibroma osificante juvenil psamomatoide maxilar. Presentación de un caso / Digital planning in the treatment of juvenile maxillary psamomatoid ossifying fibroma. Presentation of a case

Los fibromas osificantes son neoplasias fibro-óseas benignas que afectan al esqueleto craneofacial y mandibular. El fibroma osificante psamomatoide juvenil es una variante rara del fibroma osificante, la que puede ser localmente agresiva y con una alta tasa de recidiva. Se presenta el caso de una paciente de 15 años con antecedentes mórbidos de hipotiroidismo e hiperparatiroidismo, quien consulta por aumento de volumen y desplazamiento de dientes en maxilar derecho. El resultado histopatológico fue compatible con fibroma osificante psamomatoide juvenil. Dado el contexto hospitalario durante la pandemia de COVID-19, el tratamiento consistió en hemimaxilectomía con autoinjerto libre de cresta ilíaca mediante planificación digital. (AU)

Ossifying fibromas are benign fibro-osseous neoplasms that affect the craniofacial and mandibular skeleton. Juvenile psamomatoid ossifying fibroma is a rare variant of ossifying fibroma, which can be locally aggressive, and with a high recurrence rate. We present the clinical case of a 15-year-old patient with a morbid history of hypothyroidism and hyperparathyroidism, who consulted for increased volume and displacement of teeth in the right maxilla. The histopathological result was consistent with juvenile psamomatoid ossifying fibroma. Owing to the hospital situation during the COVID-19 the treatment consisted of hemimaxillectomy with iliac crest autograft using digital planning. (AU)

Juvenile ossifying fibroma of the maxillofacial region: analysis of clinico-pathological features and management / Fibroma osificante juvenil de la región maxilofacial: Análisis de características y manejo clínico-patológico

Background: The diagnosis and management of juvenile ossifying fibroma (JOF) remains a highly debated topicwith paucity of studies with long-term follow-up, hence the aim of this study was to report on the clinico-patho-logical features and management of these neoplasms.Material and Methods: A retrospective analysis was performed on all histopathologically confirmed JOF pre-senting at two tertiary hospitals in Cape Town, South Africa over a period of 39 years. Clinical, demographic,histopathological and radiological features were analyzed. Surgical methods were documented and a minimumpost-operative follow-up of 12 months was a prerequisite.Results: Seventeen patients met the inclusion criteria and were included in this study. Overall, the ages of patientsranged from 3–31 years (mean= 13 years) with male to female ratio of 1.8:1. The ages of patients diagnosed withTrabecular JOF were significantly younger than patients with Psammomatoid JOF (P = 0.01). The majority ofpatients presented with marked swelling (88.2%). Interestingly, most neoplasms occurred in the mandible (76.5%)with all Psammomatoid JOF uncharacteristically occurring in the mandible. There was only one case of Trabecu-lar JOF occurring in the sinonasal area. Most neoplasms appeared as unilocular (76.5%) and well-defined (82.4%)with mixed radio-density (70.6%) on radiographs and computed tomography. Curettage with peripheral ostectomywas shown to be the least invasive method with an acceptable recurrence rate (10%). Six lesions underwent resec-tion without any recurrences however caused high morbidity to these young patients.Conclusions: The high number of lesions occurring in the mandible for both variants of JOF demonstrates that siteshould not be a major determining factor in the diagnosis of JOF. Moreover, curettage with peripheral ostectomy...(AU)