ABSTRACT
Presently described is successful cesarean delivery in a pregnancy superimposed on long-term bosentan treatment in an Eisenmenger syndrome patient with cor triatriatum sinistrum, double-orifice mitral valve, and large ventricular septal defect resulting in single functioning ventricle with double outlets. Cesarean delivery was performed at 27th week of gestation without maternal or fetal morbidity. The infant had no congenital cardiovascular abnormality or any probable teratogenic effect of bosentan treatment during pregnancy.
Subject(s)
Cesarean Section , Cor Triatriatum/complications , Heart Septal Defects, Ventricular/complications , Infant, Extremely Premature , Sulfonamides/therapeutic use , Adult , Bosentan , Cardiovascular Agents/therapeutic use , Cor Triatriatum/drug therapy , Eisenmenger Complex/complications , Eisenmenger Complex/drug therapy , Female , Humans , Infant, NewbornABSTRACT
We present a rather unusual cause for syncope associated with atrial tachycardia. A man aged 39 years presented with an episode of syncope and narrow complex tachycardia. Further investigations, including transoesophageal echocardiography, identified cor triatriatum sinistrum (CTS), a rare congenital abnormality characterised by the atrium being divided by a fibrous membrane. Although it is rare, there has been an increase in diagnosis due to developments in diagnostic imaging techniques. Symptoms are related to the size of fenestrations within the fibrous membrane. Presenting symptoms can mimic those seen in mitral stenosis. It is a condition that can occur in isolation, but it can also be associated with other cardiac abnormalities such as an atrial septal defect (ASD) (as in this case). Surgery is the definitive treatment (this man had surgical repair of CTS and closure of ASD) and should be considered at any age if there are any associated symptoms or complications.
Subject(s)
Cor Triatriatum/complications , Cor Triatriatum/diagnosis , Syncope/etiology , Tachycardia/etiology , Adult , Cor Triatriatum/drug therapy , Heart Atria/physiopathology , Humans , MaleSubject(s)
Cor Triatriatum/complications , Cor Triatriatum/diagnostic imaging , Funnel Chest/complications , Funnel Chest/diagnostic imaging , Heart Failure/diagnostic imaging , Heart Failure/etiology , Anticoagulants/therapeutic use , Cor Triatriatum/drug therapy , Diagnosis, Differential , Diuretics/therapeutic use , Drug Therapy, Combination , Funnel Chest/drug therapy , Heart Failure/drug therapy , Humans , Male , Middle Aged , Treatment Outcome , UltrasonographySubject(s)
Cor Triatriatum/complications , Cor Triatriatum/diagnosis , Stroke/diagnosis , Stroke/etiology , Adult , Anticoagulants/administration & dosage , Cor Triatriatum/drug therapy , Diagnosis, Differential , Female , Humans , Hydroxymethylglutaryl-CoA Reductase Inhibitors/administration & dosage , Stroke/prevention & control , Treatment OutcomeABSTRACT
Cor triatriatum dexter (CTD) is an extremely rare congenital condition arising from the persistence of the right valve of the sinus venosus. It divides the right atrium (RA) into 2 separate chambers. We report a case of a 50-year-old man who had an incidental finding of CTD on transesophageal echocardiogram. An incomplete membrane of the RA was seen, and three-dimensional echocardiogram delineated the structure clearly as a triangular sail-like structure with multiple orifices and a fenestration.
Subject(s)
Cor Triatriatum/diagnostic imaging , Echocardiography, Three-Dimensional/methods , Anticoagulants/therapeutic use , Cor Triatriatum/complications , Cor Triatriatum/drug therapy , Diagnosis, Differential , Echocardiography, Transesophageal/methods , Heart Atria/diagnostic imaging , Heart Failure/complications , Humans , Incidental Findings , Male , Middle Aged , Rare DiseasesSubject(s)
Cesarean Section , Cor Triatriatum/diagnosis , Cor Triatriatum/drug therapy , Pregnancy Complications, Cardiovascular/diagnosis , Pregnancy Complications, Cardiovascular/drug therapy , Adult , Cor Triatriatum/complications , Diuretics/therapeutic use , Dyspnea/drug therapy , Dyspnea/etiology , Female , Humans , Magnetic Resonance Imaging, Cine , Mitral Valve Stenosis/etiology , Pregnancy , Premature Birth , Pulmonary Edema/drug therapy , Pulmonary Edema/etiologyABSTRACT
Cor triatriatum dexter, in which the right atrium (RA) is divided into two chambers by a membrane, is a very rare congenital abnormality. In this abnormality, there is a high incidence of associated congenital abnormalities, particularly of the right heart. We presented two men with cor triatriatum dexter. Echocardiography is discussed as a non-invasive diagnostic tool.
Subject(s)
Cor Triatriatum/diagnostic imaging , Ebstein Anomaly/diagnostic imaging , Heart Septal Defects, Atrial/diagnostic imaging , Adult , Aged , Anti-Arrhythmia Agents/therapeutic use , Cardiac Catheterization , Cor Triatriatum/drug therapy , Cor Triatriatum/therapy , Digoxin/therapeutic use , Diuretics/therapeutic use , Ebstein Anomaly/drug therapy , Heart Septal Defects, Atrial/therapy , Humans , Male , Pulmonary Veins/diagnostic imaging , Treatment Outcome , UltrasonographyABSTRACT
We present a case of asymptomatic cor triatriatum in a 65-year old male with atrial tachycardia.
