RESUMEN
We have used dual-energy x-ray absorptiometry (DXA) in evaluation and follow-up of a patient with osteopetrosis, before and after cord blood transplantation. Other methods of follow-up in such cases have been described, but the use of DXA has not previously been reported. We have shown that DXA offers a safe means of assessing disease progression, the timing of treatment, and response after therapy for osteopetrosis.
Asunto(s)
Absorciometría de Fotón , Osteopetrosis/diagnóstico , Adyuvantes Inmunológicos/uso terapéutico , Transfusión Sanguínea , Progresión de la Enfermedad , Ergocalciferoles/uso terapéutico , Sangre Fetal , Estudios de Seguimiento , Humanos , Lactante , Interferón gamma/uso terapéutico , Masculino , Osteopetrosis/tratamiento farmacológico , Osteopetrosis/terapia , Factores de Tiempo , Resultado del TratamientoRESUMEN
Broviac and Hickman catheters facilitate the care of children with cancer but provide a source of potential infection. We describe a child with a Broviac catheter who developed left-sided bacterial endocarditis in whom right-to-left atrial shunting was documented following catheter flushing. Following removal of the catheter and administration of prolonged intravenous antibiotics, recovery was complete and cardiac function returned to normal.