[Fibrous dysplasia associated with intramuscular myxoma]. / Dysplasie fibreuse associée à un myxome des parties molles.

PURPOSE OF THE STUDY: The association of fibrous dysplasia and of soft tissue myxoma is rare. The authors report a new case and discuss the underlying mechanism. CASE REPORT: A 45 years male consulted for a large painful swelling of the right gluteal muscle. The CT scan revealed the soft tissue tumor associated with a bone cyst of the right pelvic bone. The mass was removed at operation and tumoral bone tissue was curetted, there were no evidence of tissue continuity between the two lesions. The histological diagnosis was intra muscular myxoma and fibrous dysplasia. DISCUSSION: Intra muscular myxoma associated to fibrous dysplasia of bone is a rare syndrome described by Mazabraud in 1957. A review of the literature until 1995 reveals that only 17 cases of this syndrome have been reported. Intra muscular myxoma is a rare benign soft tissue tumour arising from fibroblast. Fibrous dysplasia is a hamartomatous bony disorder, which appears in mono or polyostotic forms, with or without extraskeletal manifestation. CONCLUSION: It was not possible to demonstrate a clear correlation between the two lesions. The authors suggest that myxoma result from bone mechanical disorders.

[Sequelae in the knee extensor system following graft removal for the "Mac in Jones" type procedure]. / Les séquelles survenant au niveau du système extenseur, après le prélèvement d'un transplant pour intervention de type "Mac in Jones".

PURPOSE OF STUDY: The aim of this study was to evaluate clinical and radiological sequelae following removal of part of the patellar tendon for A.C.L. reconstruction. MATERIALS AND METHODS: A consecutive and homogenous series of 100 patients operated for chronic anterior instability (66 men, 34 women; age 16 to 55 years, average: 28.5 years) was studied. The procedure involved a free patellar tendon graft harvested from the mid third of the tendon and including its bony attachments, and in particular a long strip from the patella and a strip 10 centimeters long from the rectus femoris tendon for extra-articular reconstruction. Tendon graft sites were closed. Patellae and tibial tunnels were filled with bone debris from the drilling, and the pre-patellar fascia was closed. The mean follow-up period was 35 months. pain and radiological alterations (with pre-operative X-rays as reference) were studied, particularly for: calcifications, patellar height changes using the Insall, Blackburne and Caton methods, increase in patella tip length, femoro-patellar joint alteration. RESULTS: Calcification were found in: quadriceps tendon: 24 per cent of cases (always painless), Pre-patellar: 16 per cent of cases (usually less than 5 mm), Superior patellar tendon: 47 per cent of cases (only 2 cases being painful, no unaffected tendons were painful), Inferior patellar tendon: 7 per cent of cases (1 in the mid), Tibia tunnel: 26 per cent of cases. No cases required surgical removal. Patellar tip length did not increased significantly. Patellar tendon length decreased by 1.37 mm. Patellar height measured by the Insall, Blackburne and Caton methods was not significantly affected. The femoro-patellar joint was normal in 95 per cent of cases. There were five cases of remodelling, one being painful. CONCLUSION: Graft harvested from the extension system for A.C.L. reconstruction frequently resulted in radiological sequelae but were usually asymptomatic. In most cases these calcifications concerned the superior patellar tendon, quadricipital tendon and pre-patellar zone. Patella height was not affected.

Larsen's syndrome: review of the literature and analysis of thirty-eight cases.

Thirty-eight cases of Larsen's syndrome in patients living on Reunion Island were analyzed, with an average follow-up of 13 years. Fourteen of these patients died of early complications secondary to dislocation of the cervical spine, tracheomalacias, heart disease, and severe respiratory infection. These children pose a problem of planning early treatment. Clubfeet must be treated conservatively early, and operation should be postponed until after knee deformities are corrected by plaster cast and/or early operation. Unilateral hip dislocations should be treated surgically in the second year of life. Treatment of bilateral hip dislocations is best neglected. Finally, the spinal status of these children must be monitored throughout their life.