A history of the surgical correction of pyloric stenosis.

Infantile hypertrophic pyloric stenosis (IHPS) is a complex disorder with an incidence from 4 to 5 per 1000 live births with a strongly male predilection. The natural history of this initially fatal condition with nearly 100% mortality has evolved to a disease with a good prognosis. Pyloromyotomy by Ramstedt was first described 110 years ago and still remains the standard of surgical treatment for patients with IHPS. The laparoscopic approach is becoming more common and is the preferred method of treatment now in many centres.

A milestone in congenital cardiac surgery: Four decades of the Norwood procedure.

Hypoplastic left heart syndrome (HLHS) was first described by Lev in 1952, but it was not until 1958 that it received a name from Noonan and Nadas. For the next several decades, the defect was considered untreatable. In 1979, William Norwood and his colleagues from Boston initiated a program to evaluate staged surgical management for infants with HLHS. The Norwood operation has became a milestone in the effective palliation for neonates born with HLHS. Today, the Norwood procedure is the first step of a three-stage heart surgery aimed at creating a new circulatory pathway (i.e., the Fontan pathway).

Levosimendan as a bridge to heart transplant in a 16-year-old patient with univentricular heart.

We report the successful use of levosimendan in the treatment of heart failure in a patient with the univentricular heart. The presented case was atypical because our patient had systemic right ventricle. To our knowledge, it is the first reported such case with intermittent levosimendan administration as an effective treatment and bridge to successful heart transplant in a patient with functionally univentricular heart.

Adam Christian Thebesius' Channels into the Human Heart: the Thebesian Veins and the Thebesian Valve.

In 1708, Adam Christian Thebesius, a 22-year-old student at Leiden University, presented his graduate thesis, Disputatio medica inauguralis de circulo sanguinis in corde. More than a doctoral dissertation, this groundbreaking work opened new channels into the study of the human coronary venous system. Thebesius' theory about the vascular communication between the coronary arteries and the chambers of the heart helped to advance understanding of hemodynamic principles and to clarify the physiologic pathways of the coronary circulation. The following article-the third in a trilogy about Lower Silesian scientists-provides an overview of the life story and achievements of this Silesian physician and innovator, whose name was immortalized in 2 cardiac eponyms: the Thebesian veins and the Thebesian valve.

The Visionaries, the Virtuosos, and the History of Congenital Esophageal Atresia Surgery.

The year 2018 marks the 130th anniversary of the first known surgical attempt at correction of esophageal atresia, performed by Charles Steele. But before the first successful procedure happened, many other surgeons undertook heroic attempts to save newborns and infants with this defect. Two hundred seventy-one years passed from the first description of the defect to the first surgery survivor. This paper presents a fascinating history of these milestones in pediatric surgery and of its pioneers whose creativity, mastery, and fantasy created a basis of congenital esophageal atresia surgery.

Jan Evangelista Purkinje: A Passion for Discovery.

December 2017 was the 230th anniversary of Jan Evangelista Purkinje's birth, which prompted us to review the life of this remarkable man who established the world's first department of physiology in Wroclaw and whose name is immortalized in the cardiologic eponym, Purkinje fibers. This paper offers an overview of Purkinje's life, legacy, and numerous scientific discoveries.

Usefulness of cutting balloon angioplasty for the treatment of congenital heart defects.

BACKGROUND: Patients with complex congenital heart defects may have different hemodynamic prob-lems which require a variety of interventional procedures including angioplasty which involves using high-pressure balloons. After failure of conventional balloon angioplasty, cutting balloon angioplasty is the next treatment option available. The purpose of this study was to evaluate the safety and efficacy of cutting balloon angioplasty in children with different types of congenital heart defects. METHODS: Cutting balloon angioplasty was performed in 28 children with different congenital heart defects. The indication for cutting balloon angioplasty was: pulmonary artery stenosis in 17 patients, creating or dilatation of interatrial communication in 10 patients, and stenosis of left subclavian artery in 1 patient. RESULTS: In the pulmonary arteries group there was a significant decrease in systolic blood pressure (SBP) in the proximal part of the artery from the average 74.33 ± 20.4 mm Hg to 55 ± 16.7 mm Hg (p < 0.001). Distal to the stenosis there was an increase in SBP from 19.8 ± 3.82 mm Hg to 30.3 ± ± 13.3 mm Hg (p = 0.04). This result remained constant in the follow-up. In atrial septal defect/fenestra-tion group, cutting balloon angioplasty was performed after an unsuccessful classic Rashkind procedure. After cutting balloon angioplasty there was a significant widening of the interatrial communication. CONCLUSIONS: Cutting balloon angioplasty is a feasible and effective treatment option in different con-genital heart defects.

The Two Anomalies of Wilhelm Ebstein.

The year 2016 was the 180th anniversary of Wilhelm Ebstein's birth and the 150th anniversary of his description of the congenital tricuspid valve malformation that came to be known as Ebstein anomaly. We present a brief history of the life and work of Dr. Wilhelm Ebstein. Despite his distinguished career, he is seemingly forgotten in his own birthplace. We include a review of the relevant historical medical literature.

The radiologist's tragedy, or Bland-White-Garland syndrome (BWGS). On the 80(th) anniversary of the first clinical description of ALCAPA (anomalous left coronary artery from the pulmonary artery).

In 1933, three doctors from the Massachusetts General Hospital in Boston, Paul Dudley White, William Franklin Bland, and Joseph Garland, described a case of an anomalous origin of the left coronary artery arising from the pulmonary artery (ALCAPA) in a three-month-old boy. The infant died following two weeks of hospitalization. The child's father was Dr. Aubrey Hampton, a radiologist and colleague of White, Bland, and Garland. The paper presents a perspective view on the occasion of the 80(th) anniversary of the first clinical description of ALCAPA.

[Difficult collaboration, shared eponym - Taussing-Bing syndrome]. / Trudna wspólpraca, wspólny eponim,czyli zespól Taussig−Binga.

Taussig-Bing syndrome is a rare congenital heart defect consisting of a double outlet right ventricle paired with a subpulmonic ventricular septal defect. The anomaly has first been described by collaborators Hellen Taussig and Richard Bing. In the 62 years since, much has changed in its diagnosis and treatment, but Taussig-Bing remains a challenge for congenital heart defect specialists. The biographies of the two doctors could serve as the basis for a film script. Their collaboration was not an easy one. They had difficulties with achieving consensus in professional matters, and did not like each other personally. It is amazing that today their names are mentioned together. They have been linked forever in the eponymous term for the rare heart defect they had described.

[Fallot, Blalock and Taussig - the 'blue babies' odyssey]. / Fallot, Blalock i Taussig - czyli odyseja "niebieskich dzieci"

120 years ago, Louis Fallot described a congenital heart malformation consisted of a special constellation. This was a cyanotic malformation, hence the term 'the blue baby syndrome'. In 1949 there was a first trial of correction of tetralogy of Fallot by joining pulmomary artery with subclavial artery. This vessels connection was fixed in medical terminology as Blalock-Taussig shunt.