RESUMEN
We evaluated the frequency of an association of cutaneous cervicofacial hemangiomas in a "beard" distribution (including the preauricular areas, chin, anterior neck, and lower lip) with symptomatic hemangiomas of the upper airway or subglottic areas. Of 529 patients seen, 187 were pediatric patients with hemangiomas of the head and neck. Sixteen of the 187 patients (8.5%) had cutaneous lesions with a beard distribution, with a score of 4 or greater. Ten of these 16 (63%) patients had some degree of symptomatic airway involvement, and four of the 10 (40%) required tracheotomy. The presence of cutaneous hemangiomas in a beard distribution should alert the evaluating physician to the potential association of upper airway or subglottic involvement.
Asunto(s)
Neoplasias Faciales/patología , Hemangioma/patología , Neoplasias Laríngeas/patología , Neoplasias Primarias Múltiples/patología , Adolescente , Corticoesteroides/uso terapéutico , Adulto , Niño , Preescolar , Neoplasias Faciales/tratamiento farmacológico , Neoplasias Faciales/cirugía , Femenino , Hemangioma/tratamiento farmacológico , Hemangioma/cirugía , Humanos , Lactante , Recién Nacido , Neoplasias Laríngeas/tratamiento farmacológico , Neoplasias Laríngeas/cirugía , Masculino , Neoplasias Primarias Múltiples/tratamiento farmacológico , Neoplasias Primarias Múltiples/cirugía , Estudios Retrospectivos , TraqueotomíaRESUMEN
A 13-month-old immunocompetent girl had fever, rash, and multisystem disease, and she eventually died of cardiac failure. Autopsy revealed intracellular viral inclusions of the herpesvirus group, with results of in situ hybridization positive for human herpesvirus-6. This is apparently the first case of fatal disseminated herpesvirus-6 infection.