RESUMEN
Wilms' tumor occurs rarely in adults, especially after the third decade. In adults, the prognosis of Wilms' tumor is worse than in children. In this case report, we present a 48-year old patient who relapsed with advanced stage shortly after primary surgery. A definitive treatment plan has not been established because of the rarity of this tumor in adults. After surgical removal, multimodal therapy should be begun immediately for long-lasting, complete remission.
Asunto(s)
Protocolos de Quimioterapia Combinada Antineoplásica/uso terapéutico , Neoplasias Renales/tratamiento farmacológico , Neoplasias Renales/radioterapia , Tumor de Wilms/tratamiento farmacológico , Tumor de Wilms/radioterapia , Terapia Combinada , Humanos , Neoplasias Renales/patología , Neoplasias Renales/cirugía , Masculino , Persona de Mediana Edad , Metástasis de la Neoplasia/tratamiento farmacológico , Metástasis de la Neoplasia/radioterapia , Resultado del Tratamiento , Tumor de Wilms/patología , Tumor de Wilms/cirugíaRESUMEN
We report 4 patients with xanthogranulomatous pyelonephritis (diagnosed and treated between 1992 and 1996), aged 16 to 55 years (mean age 37 years). All had urolithiasis, pyonephrosis and nonfunctioning kidneys prior to surgical intervention, and underwent total nephrectomy. Clinical, laboratory and radiologic findings are discussed in the light of the cases reported in the literature.
Asunto(s)
Riñón/patología , Pielonefritis Xantogranulomatosa/cirugía , Adolescente , Adulto , Humanos , Masculino , Persona de Mediana Edad , Nefrectomía , Pielonefritis Xantogranulomatosa/diagnósticoRESUMEN
A congenital cholesteatoma or epidermoid is a benign mass that causes devastating effects if left untreated. An unusual case with a congenital cholesteatoma located in the mastoid region complicated by epidural abscess, sinus thrombosis, and cutaneous fistula is presented. The patient had normal otologic findings and had no neurologic deficit. A review of the literature found no report of a similar case.
Asunto(s)
Absceso/etiología , Colesteatoma/congénito , Fístula Cutánea/etiología , Apófisis Mastoides/anomalías , Trombosis de los Senos Intracraneales/etiología , Absceso/diagnóstico , Absceso/cirugía , Colesteatoma/complicaciones , Colesteatoma/diagnóstico , Colesteatoma/cirugía , Fístula Cutánea/diagnóstico , Fístula Cutánea/cirugía , Espacio Epidural/patología , Espacio Epidural/cirugía , Femenino , Humanos , Apófisis Mastoides/patología , Apófisis Mastoides/cirugía , Microcirugia , Persona de Mediana Edad , Trombosis de los Senos Intracraneales/diagnóstico , Trombosis de los Senos Intracraneales/cirugía , Tomografía Computarizada por Rayos XRESUMEN
Two cases of occult spinal dysraphism with different clinical symptoms, signs and congenital pathologies are presented. One had malformations including scoliosis, dermoid tumor, hydromyelia, diastematomyelia, dermal sinus, low conus, vertebrae anomalies and dextrocardia. The occurrence of dextrocardia in association with occult spinal dysraphism was found to be extremely unusual. The second case is presented in relation to the rarity of teratoma with dermal sinus and tethered cord in the lumbar area. Myelography, computed tomography, (CT), Myelo CT and magnetic resonance were used in making a diagnosis.