RESUMEN
Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.
Asunto(s)
Humanos , Masculino , Femenino , Lactante , Atresia Biliar/diagnóstico , Enfermedades de Inicio Tardío/diagnóstico , Hígado/patología , Atresia Biliar/patología , Atresia Biliar/cirugía , Biopsia , Diagnóstico Diferencial , Arteria Hepática/patología , Enfermedades de Inicio Tardío/patología , Enfermedades de Inicio Tardío/cirugíaRESUMEN
Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.