Pulmonary agenesis with esophageal atresia and tracheoesophageal fistula.

A twin neonate with esophageal atresia, tracheoesophageal fistula, and agenesis of the right lung from consanguinous parents is reported. The twin brother was normal. The baby eventually made a good recovery after delayed primary esophageal anastomosis. Thirteen similar cases have been reported in the literature but all died.