Cardiac myxoma with prenatal diagnosis.

The presentation of myxoma in the neonatal period is quite rare. We report the case of a female patient in whom two cardiac tumors were diagnosed prenatally. Surgery was performed at eight days of age, using cardiopulmonary bypass and circulatory arrest to facilitate excision of two polypoid tumors from within the right atrium. Pathology studies were consistent with myxoma. The postoperative course was satisfactory and the patient was discharged 14 days after surgery, at 22 days old.

Mixoma cardíaco con diagnóstico prenatal: presentación de un caso y revisión de literatura / Pre-natal diagnosis of cardiac myxoma: case presentation and literature review

El mixoma es la tumoración cardíaca más frecuente en el adulto, constituyendo aproximadamente el 50% de las mismas. En la edad pediátrica el tumor cardíaco más frecuente es el rabdomioma, generalmente asociado a esclerosis tuberosa. La presentación del mixoma en pacientes pediátricos es muy rara y más aun en la etapa neonatal. Presentamos el caso de una paciente de sexo femenino que fue sometida a cirugía a los 8 días de nacida por presentar dos tumoraciones intracardiacas diagnosticadas en la etapa intrauterina a las 38 semanas de gestación. La cirugía se realizó mediante esternotomía media, con circulación extracorpórea y arresto circulatorio. Las tumoraciones, que eran de aspecto polipoide se localizaban en la aurícula derecha, los estudios de patología fueron compatibles con mixoma. La evolución postoperatoria fue satisfactoria y la paciente fue dada de alta a los 14 días después de la cirugía.

Myxoma is the most frequent cardiac tumor in adults, representing approximately 50% of the cardiac tumors. In children, the most common cardiac tumor is the rhabdomyoma, usually associated with tuberous sclerosis. Myxoma of the heart is very uncommon in children including the pre-natal period. We present here the case of a female patient who underwent heart surgery at the age of 8 days to remove two intracardiac tumors diagnosed at 38 weeks of pregnancy. The surgical procedure was performed through a median sternotomy with extracorporeal circulation and cardiac arrest. The polypoid tumors were found in the right atrium and were compatible with cardiac myxomas. Post-operative evolution was satisfactory; the patient was discharged 14 days after surgery.

Correção cirúrgica da origem anômala de artéria pulmonar direita em aorta ascendente / Surgical repair of the anomalous origin of the right pulmonary artery from the ascending aorta

A origem anômala da artéria pulmonar direita em aorta ascendente é uma malformação congênita rara. Descrevemos o caso de uma criança submetida à correção cirúrgica com anastomose direta entre a artéria pulmonar direita e o tronco pulmonar. Após 18 meses a paciente permanece assintomática sem apresentar estenose residual significativa na angioressonância.

Surgical repair of the anomalous origin of the right pulmonary artery from the ascending aorta.

The anomalous origin of the right pulmonary artery (AORPA) from the ascending aorta is a rare congenital malformation. We describe an infant who underwent a surgical correction with direct anastomosis between the right pulmonary artery and the pulmonary trunk. Eighteen months later, the patient remains asymptomatic, and no significant residual stenosis was detected on angioresonance.