Telangiectasia hemorrágica hereditaria: aspectos otorrinolaringologías / Hereditary hemorrhagic telangiectasia: ENT aspects

La telangiectasia hemorrágica hereditaria es una displasia vascular multisistémica caracterizada por el desarrollo de telangiectasias mucocutáneas y malformaciones arteriovenosas viscerales. Una de sus manifestaciones clínicas más frecuentes es la epistaxis recurrente, que se presenta en más del 90% de los pacientes, por lo que el otorrinolarin-gólogo debiera estar familiarizado con el diagnóstico y manejo de esta patología. Debido al carácter genético de la enfermedad, el manejo del sangrado nasal en estos pacientes es difícil. Existen diversas alternativas terapéuticas, farmacológicas y quirúrgicas, descritas para disminuir el número y gravedad de los episodios de epistaxis.

Hereditary hemorrhagic telangiectasia is a multisystemic vascular dysplasia, characterized by the development of mucocutaneoustelangiectasias and visceral arteriovenous malformations. One of its most frequent clinical manifestations is recurrent epistaxis, presenting in up to 90%% of these patients, so the otorhinolaryngologist should be familiarized with its diagnosis and management. Due to the genetic character of this disease, the management of nasal bleeding in these patients is difficult. There are several therapeutic alternatives, both pharmacological and surgical, described to decrease the number and severity of the episodes of epistaxis.

National linguistic validation of the Tinnitus Handicap Inventory (THI). Assessment of disability caused by tinnitus in Chilean Spanish-speaking population.

INTRODUCTION: The psycho-emotional assessment is of utmost importance for evaluation of patients with tinnitus. The Tinnitus Handicap Inventory (THI), is the most known and validated test for this purpose. OBJECTIVES: We propose a linguistic validation of the THI, in order to obtain reliable answers in our country. MATERIALS AND METHODS: We performed a translation of the original English questionnaire and assessed its feasibility by applying it in a group of patients with tinnitus. Statistical analysis included internal validity (Cronbach's alpha) and linear correlation tests (Pearson coefficient). RESULTS: We evaluated 60 patients with a mean age of 59 years. We obtained a Cronbach's alpha index of 0.97 for the whole questionnaire. CONCLUSIONS: The adapted version of the THI shows satisfactory levels of internal consistency for the assessment of disability caused by tinnitus.