[Mitochondrial monoamine oxidase in progressive Duchenne muscular dystrophy]. / Mitokhondrial'naia monoaminoksidaza pri progressiruiushchei myshechnoi distrofii Diushenna.

In children with progressive Duchenne muscular dystrophy distinct impairment in activity, of mitochondrial monoamine oxidase from skeletal muscles correlated with the step of myodystrophic process. The decrease in activity of monoamine oxidase in mitochondria of skeletal muscles, occurred with simultaneous increase in intensity of amines deamination in a medium surrounding the organelles, might de due to "leakage" of the enzyme as a result of deterioration of mitochondrial membranes permeability developed in the disease.

[Adrenergic structures and monoamine oxidase activity in dystrophic skeletal muscles]. / Adrenergicheskie struktury i aktivnost' monoaminoksidazy v distrofichnykh skeletnykh myshtsakh.

Patients with Duchenne's progressive muscular dystrophy show a high catecholamine content in the adrenergic structures and low mitochondrial monoamine oxidase activity in the skeletal muscles. Activation of dopamine deamination in the mitochondria-surrounding medium may be accounted for by the damage te mitochondrial membrane permeability. Patients with Charcot-Marie's neural amyotrophy did not manifest any such alterations.

[Effect of retabolyl on the dynamics of urinary catecholamine and DOPA excretion and electroneuromyographic indices in patients with Duchenne's myodystrophy]. / Vliianie retabolila na dinamiku urinarnoi ékskretsii katekholaminov, DOFA i élektroneiromiograficheskikh pokazatelei u bol'nykh s miodistrofiei Diushenna.

The monitoring of the use of anabolic hormones in patients with progressive Duchenne's muscular dystrophy was shown to be possible with the help of the clinical analysis of the patients' motor possibilities, electroneuromyographic examination and determination of the time-course of the urinary excretion of catecholamines and DOPA.