RESUMO
Seventy children with Down Syndrome (22 boys and 48 girls), ages ranging between five and seventeen years, were evaluated for instability of the upper cervical-spine. X-ray study of this region in lateral projection was did, in neutral position and flexion-extension of the neck. The distance between the anterior arch of the atlas and odontoid process as well as the displacement of the basion in relation to the first cervical vertebrae were examined. Twelve patients (17.14 percent) exhibited motion alterations of the region studied: atlanto-axial instability in eight cases (interval bigger than 4.5 mm) and atlanto-occipital instability in four cases.
Assuntos
Articulação Atlantoccipital/patologia , Síndrome de Down/complicações , Instabilidade Articular/etiologia , Adolescente , Articulação Atlantoccipital/diagnóstico por imagem , Criança , Estudos de Coortes , Síndrome de Down/patologia , Feminino , Humanos , Instabilidade Articular/diagnóstico por imagem , Instabilidade Articular/epidemiologia , Instabilidade Articular/patologia , Masculino , Processo Odontoide/diagnóstico por imagem , Processo Odontoide/patologia , Radiografia , Espanha/epidemiologia , Compressão da Medula Espinal/etiologiaRESUMO
The amniotic band syndrome is a collection of malformations of unclear etiopathogenesis and wide clinical significance. In this article, the characteristics of a series of eight children suffering from this syndrome are presented. Furthermore, the different aspects of the syndrome, the proposed etiologic theories, prenatal and postnatal diagnoses, and the therapeutic possibilities, from genetic counseling to surgical intervention, are discussed.
