RESUMO
We present a 19-year-old college student completely asymptomatic who underwent successful Bjork surgery (right atrium-to-right ventricle connection) in infancy with excellent results. Surgical approach for tricuspid atresia is done in three stages. Blalock Tuassig shunt soon after birth or pulmonary artery band depending on the size of the ventricular septal defect (VSD) and the main pulmonary artery, Glenn surgery (bidirectional cavopulmonary shunt) at 3-6 months of age, and Fontan surgery at 2-3 years age. There are many short- and long-term complications after Fontan surgery and patients require multiple medications throughout life. For tricuspid atresia with normally related great arteries, large VSD, and normal pulmonary valve, Bjork surgery offers the advantages of right ventricular growth, biventricular function, and good outcome without any medications.
