El síndrome de Halasz en el niño / Halasz syndrome in the child

El síndrome de Halasz es una malformación poco frecuente y con características bien definidas. Aportamos el estudio realizado en tres niños, menores de tres años, con estudio clínico, radiográfico, isotópico y hemodinámico (cateterismo y angiocardiografía) y se revisan los casos existentes en la bibliografía de pacientes menores de 15 años; se perfilan los síntomas y signos que conducen al diagnóstico y a la orientación terapéutica (AU)

[Coarctation of the aorta. In infancy (author's transl)]. / Coartación aórtica en el lactante.

We review our experience in 38 patients with coarctation of the aorta during infancy. Cardiac failure was present in 30 patients, being the maximal incidence during the first and second weeks of the life. Sixteen infants died, 43% of them during the first week. Cardiac catherization and angiocardiography were performed in 22 infants. The coarctation of the aorta was isolated in 38 infants (36%). The most frequently associated malformations were: patent ductus arteriosus (6 cases), ventricular septal defect (5 cases) and the pathology of the left heart. The post mortem examination was performed in 11 infants; in all of them the CoAo was preductal with patent ductus arteriosus; the most frequently associated malformation was ventricular septal defect (6 cases). 5 infants were operated upon with succes during the first year of the life.

[Di Giorge's syndrome with congenital heart disease (author's transl)]. / Síndrome de Di Giorge Estudio cardiológico en tres casos.

Authors describe three cases of Di Giorge's syndrome (thymic and parathyroid aplasia) proved through anatomical study postmorten, associated with cardiac malformations (Tetralogy of Fallot with pulmonary atresia, persistent truncus arteriosus and large patent ductus arteriosus). Clinical characteristics of the stated syndrome are analized with special reference to congenital heart diseases that are included in it.