Management of fibro-osseous lesions of the craniofacial area. Presentation of 19 cases and review of the literature

Introduction: Fibro-osseous lesions constitute a rare benign type of pathology with a non-odontogenic lineage that affect the craniofacial area. According to Waldrom’s classification, these lesions are divided into: fibrous dysplasia (FD), cemento-ossifying fibroma (COF) and desmoplastic fibroma (DF).Material and Methods: A retrospective study was performed on patients diagnosed with fibro-osseous lesions of the craniofacial area at the Hospital Universitario La Fe, Valencia, during 1987-2009. A total of 19 cases were collected:15 cases compatible with an FD diagnosis, 3 cases with a COF diagnosis and 1 case with a DF diagnosis. Results: In the differential diagnosis, entities having similar clinical manifestations in the maxillofacial area with possible involvement of teeth or manifestations present as an asymptomatic radiolucent image should be ruled out. We hereby present the management and development of patients treated in our hospital for fibro-osseous lesions. Conclusions: Fibro-osseous lesions share many clinical and radiological characteristics in common, with histological features confirming the nature of the lesion. Management of patients should be individualized and casespecific, assessing the clinical evolution of each case and taking into account the benign nature and growth behavior of this type of tumors (AU)

Management of fibro-osseous lesions of the craniofacial area. Presentation of 19 cases and review of the literature.

INTRODUCTION: Fibro-osseous lesions constitute a rare benign type of pathology with a non-odontogenic lineage that affect the craniofacial area. According to Waldrom's classification, these lesions are divided into: fibrous dysplasia (FD), cemento-ossifying fibroma (COF) and desmoplastic fibroma (DF). MATERIAL AND METHODS: A retrospective study was performed on patients diagnosed with fibro-osseous lesions of the craniofacial area at the Hospital Universitario La Fe, Valencia, during 1987-2009. A total of 19 cases were collected: 15 cases compatible with an FD diagnosis, 3 cases with a COF diagnosis and 1 case with a DF diagnosis. RESULTS: In the differential diagnosis, entities having similar clinical manifestations in the maxillofacial area with possible involvement of teeth or manifestations present as an asymptomatic radiolucent image should be ruled out. We hereby present the management and development of patients treated in our hospital for fibro-osseous lesions. CONCLUSIONS: Fibro-osseous lesions share many clinical and radiological characteristics in common, with histological features confirming the nature of the lesion. Management of patients should be individualized and case-specific, assessing the clinical evolution of each case and taking into account the benign nature and growth behavior of this type of tumors.

Carcinoma epitelial-mioepitelial de glándulas salivales: comportamiento, diagnóstico y tratamiento / Salivary gland epithelial-yoepithelial carcinoma: behaviour, diagnosis and treatment

Dentro de la amplia gama de la patología tumoral del área máxilo-facial y cervical, nos encontramos con aquellos tumores cuyo origen se encuentra en las glándulas salivales. Dentro de los tumores de glándula salival los subdividimos en malignos o benignos, siempre que esta subdivisión teórica sea posible. El carcinoma epitelial-mioepitelial representa aproximadamente el 1 por ciento de las neoplasias malignas de glándula salival, y puede afectar a otras regiones anatómicas en donde existan estructuras glandulares como pulmón, riñón, miometrio, etc… A partir de un caso clínico de carcinoma epitelial-mioepitelial de glándula salival menor, hacemos una revisión bibliográfica de esta infrecuente extirpe histológica. Presentamos un caso de carcinoma epitelial-mioepitelial de glándula salival menor en región geniana derecha. Se revisan las características clínicas e histológicas de este tipo de tumores relativamente poco frecuentes. Discutimos la forma de diagnóstico más correcta, el tratamiento realizado y el diagnóstico diferencial con otras lesiones con las que puede guardar gran similitud clínica (AU)