RESUMO
Teaching Point: Familial dilated cardiomyopathy (DCM) predisposes to malignant ventricular arrhythmias and sudden cardiac death, and magnetic resonance imaging (MRI) has important diagnostic value in demonstrating non-ischemic patterns of late gadolinium enhancement (LGE).
RESUMO
Left main coronary artery (LMCA) extrinsic compression should be suspected in patients with pulmonary hypertension and angina. Coronary angiography and intracoronary imaging are complementary techniques to confirm the diagnosis and guide therapy. In the largest prospective single-center series, the prevalence of a significant LMCA stenosis >50% due to dilated pulmonary artery-induced extrinsic compression was 6% in the pulmonary arterial hypertension population, and increased to 40% in patients with angina-like symptoms.