RESUMO
Abstract Clinical data: Infant, 7 months, female, referred to our department at one month of age, suspecting of congenital heart disease for further investigation. Chest radiography: Demonstrates cardiomegaly and prominent pulmonary vascular markings. Electrocardiography: Shows right ventricular hypertrophy and left anterior fascicular block. Echocardiography: Evidenced common atrioventricular valve with two orifices and the left superior pulmonary vein draining on the brachiocephalic vein. Computed tomography angiography: This complementary imaging exam was performed to confirm the diagnosis. Diagnosis: The patient presented an association between AVSD and PAPVC, a rare combination. The clinical picture of heart failure was preponderant, characterized by need for diuretics and complementary exams findings, and early surgical treatment was indicated. Operation: The operation was performed through a median sternotomy with 123 minutes of cardiopulmonary bypass and 89 minutes of cross-clamping time. The patient had no postoperative complications, remaining 10 days hospitalized.
Assuntos
Humanos , Feminino , Lactente , Anormalidades Múltiplas/diagnóstico por imagem , Malformações Vasculares/diagnóstico por imagem , Cardiopatias Congênitas/diagnóstico por imagem , Comunicação Interatrial/diagnóstico por imagem , Veias Pulmonares/anormalidades , Veias Pulmonares/cirurgia , Anormalidades Múltiplas/cirurgia , Ponte Cardiopulmonar , Eletrocardiografia , Malformações Vasculares/cirurgia , Angiografia por Tomografia Computadorizada , Cardiopatias Congênitas/cirurgia , Comunicação Interatrial/cirurgiaAssuntos
Humanos , Feminino , Lactente , Tetralogia de Fallot/complicações , Tetralogia de Fallot/diagnóstico por imagem , Síndrome de Bland-White-Garland/complicações , Síndrome de Bland-White-Garland/diagnóstico por imagem , Tetralogia de Fallot/cirurgia , Ecocardiografia , Radiografia Torácica , Resultado do Tratamento , Eletrocardiografia , Síndrome de Bland-White-Garland/cirurgia , Angiografia por Tomografia ComputadorizadaRESUMO
CLINICAL DATA: Infant, 7 months, female, referred to our department at one month of age, suspecting of congenital heart disease for further investigation. CHEST RADIOGRAPHY: Demonstrates cardiomegaly and prominent pulmonary vascular markings. ELECTROCARDIOGRAPHY: Shows right ventricular hypertrophy and left anterior fascicular block. ECHOCARDIOGRAPHY: Evidenced common atrioventricular valve with two orifices and the left superior pulmonary vein draining on the brachiocephalic vein. COMPUTED TOMOGRAPHY ANGIOGRAPHY: This complementary imaging exam was performed to confirm the diagnosis. DIAGNOSIS: The patient presented an association between AVSD and PAPVC, a rare combination. The clinical picture of heart failure was preponderant, characterized by need for diuretics and complementary exams findings, and early surgical treatment was indicated. OPERATION: The operation was performed through a median sternotomy with 123 minutes of cardiopulmonary bypass and 89 minutes of cross-clamping time. The patient had no postoperative complications, remaining 10 days hospitalized.