Epidermolysis bullosa with clinical manifestations of sepsis and pneumonia: A case report.

BACKGROUND: Epidermolysis bullosa is an inherited disease that causes bleeding blisters on the skin tissues and mucosal membranes. This study reports a case of epidermolysis bullosa with clinical manifestations of sepsis and pneumonia. CASE REPORT: A 17-month-old female with epidermolysis bullosa presented with clinical manifestations of sepsis and pneumonia, including increased body temperature, anorexia, and wheezing. Blood test results included the following: white blood cell (WBC) count, 24,000/µl; hemoglobin level, 7.9 mg/dl; erythrocyte sedimentation rate (ESR), 99 mm/h; and C-reactive protein level, +2. The patient was given ceftriaxone, vancomycin, hydrocortisone, and acetaminophen. The patient's fever resolved on the third day of hospitalization, and the ESR and WBC count reached 25 mm/h and 9900/µl, respectively. CONCLUSIONS: According to the report, it is recommended to consider an increase in body temperature, WBC count, and ESR, and perform the required attempts in patients with epidermolysis bullosa.

O efeito do treinamento multimídia na função social de pacientes queimados no Hospital Shahid Motahhari, Teerã: um estudo clínico / The effect of multimedia training on social function of burned patients in Shahid Motahhari Hospital, Tehran: A clinical trial study

Introdução: a queimadura é uma lesão tecidual que afeta o convívio social e os relacionamentos. Complicações de queimaduras levam à ruptura das relações sociais e, consequentemente, à disfunção social. Objetivo: este estudo objetiva determinar o efeito do treinamento multimídia no comportamento social de pacientes queimados no hospital Shahid Motahhari em Teerã. Métodos: este estudo clínico investigou 100 pacientes queimados. O grupo de intervenção recebeu, na alta hospitalar, um treinamento de autocuidados em multimídia num CD, além das informações de rotina. A função social da qualidade de vida foi examinada em ambos os grupos antes da intervenção, três meses e seis meses após a intervenção. Conclusões: os resultados mostraram que, antes da intervenção, o escore médio da função social da qualidade de vida no grupo intervenção e controle foi de 1/55 ± 0/46 e 1/92 ± 0/6, respectivamente, o que foi estatisticamente significativo (p<0,001). A média e o desvio-padrão da função social da qualidade de vida nos grupos intervenção e controle três e seis meses após a intervenção foram 2/47±0/56, 4/05±0/77, 2/15±0/39 e 29/3±0/95, respectivamente, também estatisticamente significativo (p<0,001)

Introduction: Burn is a tissue injury and affects social functioning and relationships. Complications of burns lead to disruption of social relationships and, consequently, social dysfunction. Objective: This study aims to determine the effect of multimedia training on burned patients' social functioning in Shahid Motahhari hospital in Tehran. Methods: This clinical trial study assessed 100 burned patients. The intervention group received multimedia self-care discharge training on a CD in addition to the standard education. The social function of the quality of life was examined in both groups before the intervention, 3 months and 6 months after the intervention. Conclusions: Results showed that before the intervention, the mean score of social function of quality of life in intervention and control group was 1/55± 0/46, 1/92± 0/6, respectively, which was statistically significant (p <0.001). Mean and standard deviation of social function of quality of life in the intervention and control groups three and six months after intervention were2/47± 0/56, 4/05± 0/77, 2/15±0/39, 3/29 ± 0/95, also statistically significant (p<0.001).