RESUMO
Orbital cysticercosis is a rare condition. We report here 3 cases with orbital cysticercosis who presented with proptosis and ptosis (Case no. 1 and 2) and focal seizures (Case no. 3). All of them had a vision of 6/6. Diagnosis of cysticercosis was made on CT Scan. The lesions isolated in Cases 1 and 2 and were excised. Drug therapy was given to treat any persisting infestation. Case no 3 had multiple brain cysticerci in addition to the orbital one. However, the patient was lost to follow-up.
Assuntos
Cisticercose/diagnóstico por imagem , Doenças Orbitárias/diagnóstico por imagem , Adolescente , Adulto , Albendazol/uso terapêutico , Criança , Terapia Combinada , Cisticercose/complicações , Cisticercose/tratamento farmacológico , Cisticercose/cirurgia , Diagnóstico Diferencial , Feminino , Humanos , Niclosamida/uso terapêutico , Doenças Orbitárias/complicações , Doenças Orbitárias/tratamento farmacológico , Doenças Orbitárias/cirurgia , Tomografia Computadorizada por Raios XAssuntos
Países em Desenvolvimento , Hospedeiro Imunocomprometido/imunologia , Meningite Criptocócica/imunologia , Infecções Oportunistas/imunologia , Infecções Oportunistas Relacionadas com a AIDS/diagnóstico , Infecções Oportunistas Relacionadas com a AIDS/tratamento farmacológico , Infecções Oportunistas Relacionadas com a AIDS/imunologia , Cryptococcus neoformans/efeitos dos fármacos , Fluconazol/uso terapêutico , Humanos , Índia , Meningite Criptocócica/diagnóstico , Meningite Criptocócica/tratamento farmacológico , Infecções Oportunistas/diagnóstico , Infecções Oportunistas/tratamento farmacológicoRESUMO
Machado-Joseph-Azorean (MJA) disease is an autosomal-dominant multisystem motor degeneration (with cerebellar ataxia as an important manifestation) that is seen mainly in people of Portuguese descent. Recently, a family in Japan with probable MJA disease has been described. We describe a family with clinical features similar to those of MJA disease; these are the first cases to be described in India. Further pathologic study is necessary to confirm the diagnosis in our cases. Meanwhile, further search for such cases in India should yield interesting genetic clues to the disease.