RESUMO
A 9-year-old boy presented with the numbness in both arms and hands, and neck stiffness. On examination, he had a slight quadriparesis and restricted neck movements. There were no signs of von Recklinghausen's disease. Magnetic resonance imaging (MRI) scan disclosed a gadolinium enhanced intramedullary tumor located at C6-T1 associated with syringomyelia. C6-T1 laminectomies were performed and the intramedullary tumor was totally removed by a microsurgical technique. Postoperative course was uneventful. The pathological examination revealed an intramedullary schwannoma. The occurrence of intramedullary schwannoma in a patient without signs of von Recklinghausen's disease is extremely rare. We have been able to find 57 cases of intramedullary schwannoma reported in the literature. Intramedullary schwannomas are usually seen in males. The ages of the patients ranged from 9 to 75 years (mean 40.44 years). Only 4 cases in the pediatric age group have been reported. The duration of symptoms ranged from 3 months to 20 years (mean 31.03 months). Symptoms and signs varied with the location of tumor. The vertebral levels of intramedullary schwannomas were usually cervical (61%). MRI has been the choice of diagnostic tool in the cases reported since 1986. The majority of the cases showed either a partial or complete recovery in the postoperative period.
Assuntos
Neurilemoma/patologia , Neoplasias da Medula Espinal/patologia , Criança , Humanos , Imageamento por Ressonância Magnética , Masculino , Degeneração Neural/patologia , Neurilemoma/cirurgia , Células de Schwann/patologia , Neoplasias da Medula Espinal/cirurgiaRESUMO
A case of occipital ossifying fibroma in a 13-year-old girl is presented. Ossifying fibroma is a rare, benign, primary bone tumour that occurs most commonly in the mandible. Cranial vault location is extremely rare. To our knowledge, our patient is the second case of occipital location reported. Total surgical excision is the treatment of choice.
Assuntos
Fibroma Ossificante/diagnóstico por imagem , Osso Occipital/diagnóstico por imagem , Neoplasias Cranianas/diagnóstico por imagem , Adolescente , Craniotomia , Diagnóstico Diferencial , Feminino , Fibroma Ossificante/patologia , Fibroma Ossificante/cirurgia , Humanos , Osso Occipital/patologia , Osso Occipital/cirurgia , Osteoblastos/patologia , Radiografia , Neoplasias Cranianas/patologia , Neoplasias Cranianas/cirurgiaRESUMO
The incidence of dumbbell tumors among spinal neoplasms is between 10% and 15%. Approximately 1% of neoplasms located at or near the spinal cord are ganglioneuromas. Ganglioneuromas are rare, slow-growing, benign tumors arising from sympathetic ganglia. The cases of two children with spinal dumbbell ganglioneuroma are presented. The tumors were totally resected by combined surgery in both patients. The patients are neurologically intact 5 and 4 years respectively after surgery.
