RESUMO
Primary pulmonary synovial sarcoma is an extremely rare tumor with an unknown cause. The diagnosis is established after other primary lung malignancies or metastatic extrathoracic sarcoma have been excluded. We report the case of a 69-year-old man who presented with a well-defined mass in the right upper lobe on a chest X-ray. A video-assisted thoracoscopic surgery (VATS) right upper lobectomy was performed. Immunohistochemically, neoplastic cells were positive for vimentin, CD56 and Bcl-2, and focally positive for CD99, epithelial membrane antigen and cytokeratin 7 and 19. The cytogenetic study revealed a SYT genetic reassortment. So, the final pathological diagnosis was primary pulmonary synovial sarcoma.
RESUMO
Liposarcoma is a malignant neoplasm of mesodermal origin derived from adipose tissue. It most often originates in the extremities and retroperitoneum, and less frequently in the head and neck. Liposarcoma involving the chest wall is extremely rare with few reported cases. Surgery is the mainstay of treatment, and complete resection is the major factor influencing survival. We describe the case of a 65-year-old man diagnosed with a dedifferentiated liposarcoma of the chest wall, who underwent radical resection and chest wall reconstruction with a latissimus dorsi musculocutaneous flap.
Assuntos
Lipossarcoma/cirurgia , Procedimentos de Cirurgia Plástica/métodos , Neoplasias Torácicas/cirurgia , Procedimentos Cirúrgicos Torácicos/métodos , Parede Torácica/cirurgia , Idoso , Humanos , Lipossarcoma/diagnóstico , Imageamento por Ressonância Magnética/métodos , Masculino , Retalhos Cirúrgicos , Neoplasias Torácicas/diagnóstico , Parede Torácica/diagnóstico por imagem , Parede Torácica/patologia , Tomografia Computadorizada por Raios X/métodosRESUMO
Angiosarcomas are a rare type of malignant vascular tumour characterised by proliferation of tumour cells with vascular endothelial features. These tumours are usually very aggressive and overall mortality is very high. Pulmonary angiosarcomas are usually secondary tumours, and only a few primary cases have been reported. We present a case of a 56 year-old male with persistent haemoptysis secondary to lung epithelioid angiosarcoma with pleural metastases.