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Pediatr Cardiol ; 30(3): 352-5, 2009 Apr.
Artigo em Inglês | MEDLINE | ID: mdl-19005718

RESUMO

Plastic bronchitis is an uncommon condition characterized by the production of large pale bronchial casts that obstruct the tracheobronchial tree. The cellular content, cohesiveness, and often rubber-like consistency distinguish bronchial casts from the usual mucus plugs found with such disease states as asthma. Plastic bronchitis can be found secondary to many conditions, and a simplified classification scheme organizes it into two groups: an inflammatory type consisting of casts with an eosinophilic inflammatory infiltrate and an acellular type with a predominance of fibrin distinguished by its relative lack of cellular infiltrate, its mucin predominance, and its appearance only in children with congenital cyanotic heart disease. This report describes a 5-year-old girl who experienced plastic bronchitis 3 months after a Fontan procedure for hypoplastic left heart syndrome that was treated successfully with aerosolized tissue plasminogen activator.


Assuntos
Bronquite/tratamento farmacológico , Fibrinolíticos/administração & dosagem , Técnica de Fontan/métodos , Síndrome do Coração Esquerdo Hipoplásico/cirurgia , Ativador de Plasminogênio Tecidual/administração & dosagem , Administração por Inalação , Bronquite/diagnóstico , Bronquite/etiologia , Broncoscopia , Pré-Escolar , Diagnóstico Diferencial , Feminino , Humanos , Síndrome do Coração Esquerdo Hipoplásico/complicações , Síndrome do Coração Esquerdo Hipoplásico/diagnóstico , Radiografia Torácica
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