Condrosarcoma laríngeo: controversias diagnosticoterapéuticas / Chondrosarcomas of the larynx: diagnostic and therapeutic controversies

Los condrosarcomas laríngeos son neoplasias poco frecuentes que suponen solamente un pequeño porcentaje de todos los tumores primarios de la laringe y que ha sido estimado en menos de un 2%. Con frecuencia, la clínica que presentan es anodina pese a su progresivo crecimiento hasta que la funcionalidad de la laringe se ve severamente comprometida. Esta neoplasia se caracteriza por una agresividad local variable y frecuentes metástasis, que comúnmente se localizan en pulmones y hueso, dependiendo del tipo histológico. Presentamos un caso de un condrosarcoma laríngeo agresivo con enfermedad metastásica exclusivamente cerebral como causa de muerte, hecho extremadamente infrecuente en estos tumores. Aportamos, además, una revisión de la literatura, analizando especialmente las controversias sobre el manejo de esta entidad

Chondrosarcomas of the larynx are rare neoplasms that account only for a very small percentage of all the primary laryngeal neoplasms that has been estimated in less than 2%. They often show initially with indolent symptoms despite their progressive growth until great compromise ofthe laryngeal function is produced. This neoplasm is characterised by a variable local aggressive behaviour and frequent of distant metastasis, that are commonly located in lungs and bone, deppending on the hystologic grade. A case of an aggressive laryngeal chondrosarcoma with exclusive brain metastasic disease as cause of death, a very uncommon event in these neoplasms, is reported. We also provide a review ofthe literature focusing on the controversies about the management of tlIis condition

[Chondrosarcomas of the larynx: diagnostic and therapeutic controversies]. / Condrosarcoma laríngeo: controversias diagnosticoterapéuticas.

Chondrosarcomas of the larynx are rare neoplasms that account only for a very small percentage of all the primary laryngeal neoplasms that has been estimated in less than 2%. They often show initially with indolent symptoms despite their progressive growth until great compromise of the laryngeal function is produced. This neoplasm is characterised by a variable local aggressive behaviour and frequent of distant metastasis, that are commonly located in lungs and bone, deppending on the hystologic grade. A case of an aggressive laryngeal chondrosarcoma with exclusive brain metastasic disease as cause of death, a very uncommon event in these neoplasms, is reported. We also provide a review of the literature focusing on the controversies about the management of this condition.