RESUMO
El tumor miofibroblástico inflamatorio es un tumor raro. Su localización más habitual es el pulmón. Se han descrito otras localizaciones extrapulmonares, siendo el mesenterio y el retroperitoneo las más frecuentes. Presentamos un caso de una niña de 8 años con un tumor miofibroblástico inflamatorio en una localización inusual. La paciente fue derivada a nuestro centro por sospecha de un proceso apendicular complicado. Se realizó una ecografía abdominal en la que se detectó una invaginación de íleon terminal, con una tumoración en su extremo distal. En la intervención urgente se confirmó una invaginación de íleon distal, secundaria a una tumoración intraluminal. El resultado anatomopatológico final fue de tumor miofibroblástico inflamatorio. El tumor miofibroblástico inflamatorio es un tumor mesenquimal raro, que afecta con mayor frecuencia a niños. Cuando se localiza en el abdomen, puede simular lesiones malignas, como linfoma, sarcoma o metástasis. Su etiología y pronóstico son inciertos (AU)
Inflammatory myofibroblastic tumor is a rare lesion that is usually located in the lung. The most commonly reported extrapulmonary locations are the mesentery and the retroperitoneum. We report the case of an 8-year-old girl with an inflammatory myofibroblastic tumor in an unusual location. The patient was referred to our center for suspected complicated appendicitis. Abdominal ultrasonography detected ileoileal intussusception with a mass in the distal portion. Emergency laparotomy confirmed ileoileal intussusception secondary to an intraluminal tumor. Histologic study revealed the mass was an inflammatory myofibroblastic tumor. Inflammatory myofibroblastic tumors are rare mesenchymal masses usually found in children. When located in the abdomen, they can mimic malignant lesions like lymphomas, sarcomas, or metastases. The cause and prognosis of inflammatory myofibroblastic tumors are unknown (AU)
Assuntos
Humanos , Feminino , Criança , Intussuscepção/complicações , Intussuscepção/diagnóstico , Neoplasias de Tecido Muscular/complicações , Neoplasias de Tecido Muscular/diagnóstico , Obstrução Intestinal/complicações , Obstrução Intestinal , Imuno-Histoquímica/métodos , Intussuscepção/fisiopatologia , Intussuscepção , Neoplasias de Tecido Muscular , Abdome , Anastomose Cirúrgica/métodosRESUMO
Inflammatory myofibroblastic tumor is a rare lesion that is usually located in the lung. The most commonly reported extrapulmonary locations are the mesentery and the retroperitoneum. We report the case of an 8-year-old girl with an inflammatory myofibroblastic tumor in an unusual location. The patient was referred to our center for suspected complicated appendicitis. Abdominal ultrasonography detected ileoileal intussusception with a mass in the distal portion. Emergency laparotomy confirmed ileoileal intussusception secondary to an intraluminal tumor. Histologic study revealed the mass was an inflammatory myofibroblastic tumor. Inflammatory myofibroblastic tumors are rare mesenchymal masses usually found in children. When located in the abdomen, they can mimic malignant lesions like lymphomas, sarcomas, or metastases. The cause and prognosis of inflammatory myofibroblastic tumors are unknown.
