[Fibrous dysplasia of the skull: neurologic manifestations]. / Displasia fibrosa do crânio: manifestações neurológicas.

The neurological manifestations of eight patients with osseous fibrous dysplasia of skull were retrospectively studied. In this series, the frontal bone was involved in 75% of the patients, the sphenoid or temporal bones in 37.5%, and the parietal in 25%. It was observed that cranial deformities occurred in all but one case, headache was present in 87.5% of the patients, visual disturbances in 50%, proptosis in 25%, and auditive symptoms in 12.5%. Six out of the eight patients were operated on: three of the four who presented progressive visual loss had postoperative improvement. In their follow up, none presented, until now, evidence of recurrence or worsening of symptoms, confirming the benign nature of fibrous dysplasia.

[Neurocryptococcosis in childhood. Report of 3 cases in the 1st decade of life]. / Neurocriptococose na infância. Relato de três casos na primeira décade de vida.

The authors report three cases of central nervous system cryptococcosis in children in the first decade of life, from Rio Grande do Sul State, Brazil. Diagnosis was supported by demonstration of Cryptococcus neoformans with India-ink preparations of the spinal fluid and Sabouraud's media culture. Clinical presentation included acute, subacute and chronic forms. Increased intracranial pressure and hydrocephalus were the complications during the course of the disease, and a ventriculoperitoneal shunt was used in one case. Undernutrition was associated with all cases and tubercle bacillus infection with one. Specific therapy was administered to the three patients. One patient was cured and the other two died.

[Neurocutaneous melanosis: autopsy study of a case]. / Melanose neurocutânea: estudo autópsico de um caso.

The clinical, radiological and autopsy features of a 5-month-old child with neurocutaneous melanosis are described. The patient had multiple disseminated benign cutaneous nevi. The pneumoencephalogram showed non-obstructive hydrocephalus. The patient died at the third day of hospitalization and autopsy was performed. A mild hydrocephalus and melanic specks in cerebellum and in the brainstem were disclosed.

Hematomas intracranianos traumaticos agudos. / Acute traumatic intracranial hematoma

Os autores estudam 252 casos de hematomas intracranianos, numa casuistica de 2.700 vitimas de traumatismo craniencefalico internados no Hospital de Pronto Socorro Municipal de Porto Alegre, no periodo de outubro de 1971 a dezembro de 1980. Comentam os achados clinicos e radiologicos e discutem a incidencia, localizacao e evolucao dos hematomas intracranianos

Transfusao de sangue contaminado. / Contaminated blood transfusion

Relatamos o caso de um lactentes de dois meses e quinze dias de vida, internado em uma clinica por bronquiolite onde recebeu uma transfusao mal indicada de globulos vermelhos concentrados e que desafortunadamente estavam contaminados. Esta crianca apresentava quadro grave de septicemia por Pseudomonas aeruginosa a internacao no IPPMG. Tratando-se de uma latrogenia, sem resposta ao tratamento antimicrobiano convencional, usamos com septicemia, com bons resultados e sem efeitos colaterais. Apos introducao da Propsonina houve melhora progressiva do quadro clinico, indicando que seu uso foi importante para evolucao, cura e prognostico

[Hemorrhage in intracranial metastases of melanoma. Report of 2 cases]. / Hemorragias em metástases intracranianas de melanoma. Registro de dois casos.

Two cases of intra-cerebral haemorrhage secondary to malignant melanoma metastasis are reported. When dealing with subarachoid haemorrhages, one should think of brain secondaries and a biopsy should always be performed whenever a spontaneous intra-cerebral hematoma is found.

[Thyrotoxic periodic paralysis. Report of a case]. / Paralisia periódica tireotóxica. Registro de um caso.

A case of thyrotoxic periodic paralysis based on clinical grounds, laboratory data and therapeutic response as well is reported. The authors comment on the differential diagnosis with the most frequent types of periodic paralysis. The importance of a correct diagnosis and treatment as early as possible is stressed as to prevent further development of permanent paralysis due to irreversible degenerative myofibril changes as stated in literature.

[Intracranial tumors in childhood. Study of 106 cases]. / Tumores intracranianos na infäncia. Estudo de 106 casos.

The authors analyze 106 intracranial tumors occurring in patients from 0 to 15 years of age. This study was carried on during the period from 1962 up to 1977. In 85 cases the diagnostic work up was made on clinical, radiological, and histological grounds; the remaining 21 cases had their diagnosis based solely on clinical and radiological evidence. Observations involving incidence according to age, sex, localization and histological types are made. The signs and symptoms and supplementary examination are discussed. The frequency of primary intracranial tumors in children under 1 year of age is stressed.

[Bilateral cerebral mycotic aneurysm in a child. Report of a case and review of the literature]. / Aneurisma micótico cerebral bilateral em crianca. Registro de um caso e revisão da literatura

The case of a 6 year-old boy, who was hospitalized with the diagnosis of purlent meningits is reported. The CSF examination disclosed pleocytosis and the antibioticotherapy was instituded. The bilateral carotid angiography demonstrated an arterial aneurysm of the frontal ascendent artery with hematoma in the left side and another in the posterior temporal artery, in the right side. The patient was operated on because of the hematoma, in the left side. The condition of the patient in the post-operatory period deteriorated and the death ocurred. The post-mortem examination disclosed a sub-arachnoidal hemorrhage, fronto-temporal hematoma in the left side and a para-capsular hematoma in the right side. The histological examination of the central part of the right side. The histological examination of the central part of the hematoma revealed a dilated arterial walls with a supurative inflammatory process.