Association of the family environment with behavioural and cognitive outcomes in children with chromosome 22q11.2 deletion syndrome.

BACKGROUND: Children with 22q11.2 deletion syndrome (22q11DS) are at risk for social-behavioural and neurocognitive sequelae throughout development. The current study examined the impact of family environmental characteristics on social-behavioural and cognitive outcomes in this paediatric population. METHOD: Guardians of children with 22q11DS were recruited through two medical genetics clinics. Consenting guardians were asked to complete several questionnaires regarding their child's social, emotional and behavioural functioning, as well as family social environment and parenting styles. Children with 22q11DS were asked to undergo a cognitive assessment, including IQ and achievement testing, and measures of attention, executive function and memory. RESULTS: Modest associations were found between aspects of the family social environment and parenting styles with social-behavioural and cognitive/academic outcomes. Regression models indicated that physical punishment, socioeconomic status, parental control and family organisation significantly predicted social-behavioural and cognitive outcomes in children with 22q11DS. CONCLUSION: Characteristics of the family social environment and parenting approaches appear to be associated with functional outcomes of children with 22q11DS. Understanding the impact of environmental variables on developmental outcomes can be useful in determining more effective targets for intervention. This will be important in order to improve the quality of life of individuals affected by 22q11DS.

Academic response rate as a function of teacher- and self-imposed contingencies.

The purpose of this study was to assess the effects of the contingency manager (teacher or pupil) on a pupil's academic response rate. The results of two such experiments disclosed that higher academic rates occurred when the pupil arranged the contingency requirements than when the teacher specified them. A third study manipulated only reinforcement magnitude to ascertain whether amount of reinforcement had interacted with pupil-specified contingencies to produce the increase in academic response rate. The latter findings revealed that the contingency manager, not reinforcement magnitude, accounted for this subject's gain in performance.

Effects of manipulating an antecedent event on mathematics response rate.

The purpose of this investigation was to assess the effects on performance rate of simply writing the answers to mathematics problems versus verbalizing the problems before making a written response. The subject was an 11-yr-old boy whose response accuracy on mathematics problems was very erratic. Three experiments were conducted, each consisting of three phases. In each first phase, the subject was requested to write the answers to sets of mathematics problems. In the second, he was required to verbalize the problem before writing the answer. In the third phase, the subject was told to write the answer again without prior verbalization. The results indicated that the subject's correct answer rate increased and his error rate decreased as a result of his verbalizing the problems before making a written response. Results further revealed that in the final phase of each experiment, the return to the original conditions, his correct answer rate continued to increase.