Assuntos
Actinomicose/complicações , Antibacterianos/uso terapêutico , Dispositivos Intrauterinos/microbiologia , Doença Inflamatória Pélvica/complicações , Insuficiência Renal/etiologia , Actinomyces/isolamento & purificação , Actinomicose/tratamento farmacológico , Actinomicose/cirurgia , Feminino , Humanos , Dispositivos Intrauterinos/efeitos adversos , Pessoa de Meia-Idade , Doença Inflamatória Pélvica/tratamento farmacológico , Doença Inflamatória Pélvica/cirurgia , Insuficiência Renal/tratamento farmacológico , Insuficiência Renal/cirurgia , Resultado do TratamentoAssuntos
Doença de Paget Extramamária/terapia , Neoplasias Cutâneas/terapia , Idoso , Idoso de 80 Anos ou mais , Protocolos de Quimioterapia Combinada Antineoplásica/uso terapêutico , Diagnóstico Diferencial , Feminino , Humanos , Terapia a Laser , Masculino , Pessoa de Meia-Idade , Neoplasias Primárias Múltiplas/diagnóstico , Doença de Paget Extramamária/etiologia , Doença de Paget Extramamária/patologia , Fotoquimioterapia/métodos , Prognóstico , Neoplasias Cutâneas/etiologia , Neoplasias Cutâneas/patologiaRESUMO
BACKGROUND: Malignant hemangiopericytoma (MHPC) is a rare vascular tumor and has been reported to occur in the musculature of the extremities, retroperitoneum and pelvis. Omental hemangiopericytomas (HPCs) are extremely rare. Synovial sarcomas and solitary fibrous tumors share histologic features with HPCs, causing diagnostic difficulties. Immunohistochemistry is essential for the diagnosis. CASE: A 74-year-old woman presented with an abdominopelvic mass. A malignant ovarian tumor was suspected on clinical features, ultrasound and computed tomography. Staging laparotomy revealed a large, vascular tumor adherent to loops of small bowel, colon, cecum and appendix, but the ovaries and uterus were normal. The tumor was completely removed after extensive dissection. Histopathology and detailed immunohistochemistry established the diagnosis of a malignant hemangiopericytoma arising from the omentum. The patient developed recurrent subacute bowel obstruction and died 4 months after the initial diagnosis. CONCLUSION: MHPCs are rare tumors and not likely to be diagnosed preoperatively. Treatment is therefore individualized and based on the findings at laparotomy. Some tumors, such as the one described here, exhibit very aggressive behavior.