RESUMO
We present the results of the registry of patients of the Cuban Commission of Cystic Fibrosis up to December, 1977. 228 patients from 192 families are reported; 81.58% were Whites and 3% were Negroes. There was no sex difference in incidence. Respiratory manifestations at diagnosis were presnet in 93% of the C.F. patients. The initial Shwachman's score were of "severe" or "moderate" in one third of the patients to whom they were made. Our Commission has followed 205 patients, one third of them died and out of the rest, we consider that 64% has a good outlook; approximately 10% has poor outlook and 26% has an uncertain prognosis. All this having in mind that the Shwachman's score, in a broad sense, has been useful to establish the prognosis. The most frequent findings in the dead pateints to whom autopsies were performed were in the lungs, the pancreas and the liver. It was observed that the lower the initial score, the lower the survival.
