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Artigo em Coreano | WPRIM (Pacífico Ocidental) | ID: wpr-122485

RESUMO

Multiple endocrine neoplasia type2a (MEN type2a) is a dominantly inherited cancer syndrome which is characterized by medullary thyroid carcinoma, pheochromocytoma and parathyroid hyperplasia or adenoma. Recent reports show that DNA analysis will be introduced into screening of MEN type2a families. Regular prospective screening and appropriate surgical intervention can reduce the morbidity and mortality due to MEN type2a. We experienced a case of MEN type 2a in a 46-year-old female patient. She had undergone bilateral adrenalectomy due to pheochromocytoma, followed by a total radical thyroidectomy, which revealed medullary thyroid carcinoma of the both thyroid gland and parathyroid hyperplasia.


Assuntos
Feminino , Humanos , Masculino , Pessoa de Meia-Idade , Adenoma , Adrenalectomia , DNA , Hiperplasia , Programas de Rastreamento , Mortalidade , Neoplasia Endócrina Múltipla Tipo 2a , Neoplasia Endócrina Múltipla , Feocromocitoma , Glândula Tireoide , Neoplasias da Glândula Tireoide , Tireoidectomia
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