RESUMO
Pleomorphic adenomas of the external auditory canal (EAC) are benign tumors of the ceruminal glands; they are a rare entity. Arising from the lateral cartilaginous portion of the EAC, these lesions can be challenging to diagnose in view of their rare clinical presentation, indolent symptoms, and a lack of familiarity on the part of histopathologists. We report the case of a pleomorphic adenoma in a 32-year-old woman, and we review the literature on glandular neoplasms of the EAC, with particular emphasis on terminology and factors that can hinder the diagnosis.
Assuntos
Adenoma Pleomorfo/patologia , Orelha Externa/patologia , Neoplasias das Glândulas Salivares/patologia , Adulto , Feminino , Humanos , Invasividade NeoplásicaRESUMO
Congenital anomalies of the right main bronchi have not been fully described. Bronchial anomalies are usually asymptomatic unless they coexist with other abnormalities. We describe a rare bronchial anomaly in a 2-month-old girl in which the right upper lobe, middle lobe, and lower lobe bronchi all originated at the same point as a result of a developmental teratogenic long right main bronchus and an absent bronchus intermedius. Furthermore, the left main bronchus contained a proximal segment of stenosis. This combination of anomalies, along with right upper lobe atelectasis and left-sided hyperinflation, resulted in a severe right mediastinal shift and respiratory distress. The mediastinum was returned to midline with endoscopic placement of an in-dwelling tracheobronchial stent into the left main bronchus. To the best of our knowledge, the specific developmental anomaly in our patient has not been previously described.
Assuntos
Brônquios/anormalidades , Broncopatias/congênito , Doenças em Gêmeos , Stents , Broncopatias/terapia , Broncoscopia , Constrição Patológica/congênito , Constrição Patológica/terapia , Desenho de Equipamento , Feminino , Humanos , Lactente , Recém-Nascido , Intubação Intratraqueal/instrumentação , Síndrome do Desconforto Respiratório do Recém-Nascido/etiologia , Síndrome do Desconforto Respiratório do Recém-Nascido/terapia , Sons Respiratórios/etiologia , Traqueostomia/instrumentaçãoRESUMO
Fetal rhabdomyoma is not generally considered part of nevoid basal cell carcinoma syndrome. However, a review of the literature revealed five patients with this syndrome who also had fetal rhabdomyomas in various locations. We report the first patient with nevoid basal cell carcinoma syndrome and a fetal rhabdomyoma of the tongue. We recommend that embryonal rhabdomyosarcoma be ruled out to avoid overly aggressive treatment of these patients.
Assuntos
Síndrome do Nevo Basocelular/complicações , Rabdomioma/complicações , Neoplasias da Língua/complicações , Humanos , Recém-Nascido , Masculino , Rabdomioma/congênito , Rabdomioma/patologia , Neoplasias da Língua/congênito , Neoplasias da Língua/patologiaRESUMO
Lipoblastoma is a rare benign tumor that occurs primarily in children younger than 3 years of age. Fewer than 100 cases have been reported in the literature, and only eight cases have been previously reported in the head and neck; two of them occurred in the parotid region, where the differential diagnosis becomes quite extensive. We report a new case of head and neck lipoblastoma--one that occurred in the parapharyngeal space, a site that has not been previously reported. By doing so, we hope to promote awareness and consideration of lipoblastoma in the differential diagnosis of deep-parotid and parapharyngeal-space neoplasms.
