RESUMO
IgG4-related disease (IgG4-RD)is a multifactorial and systemic immune-mediated disease. Pulmonary vein stenosis related to IgG4 is a rare entity. We report a case of a 57-year-old male who presented with vague symptoms of weakness, easy fatigue, shortness of breathing, chest tightness, and occasional palpitations. The patient was admitted, and investigations were arranged in the form of anterior mediastinotomy and pleural biopsies were taken to look for a possible diagnosis. The histopathology was reported as IgG4-related immunopathy. A transoesophageal echocardiogram was performed and this showed severe stenosis of left superior pulmonary vein. In patients with rare pathologies such as IgG4-RD, a transesophageal can be a useful diagnostic aid especially in patients with severely impaired renal functions which does not allow utilization of contrast computed tomography.
Assuntos
Doença Relacionada a Imunoglobulina G4/diagnóstico , Estenose de Veia Pulmonar/diagnóstico , Idoso , Ecocardiografia Transesofagiana , Humanos , Doença Relacionada a Imunoglobulina G4/diagnóstico por imagem , Doença Relacionada a Imunoglobulina G4/patologia , Masculino , Índice de Gravidade de Doença , Estenose de Veia Pulmonar/diagnóstico por imagem , Estenose de Veia Pulmonar/patologiaAssuntos
Neoplasias das Glândulas Suprarrenais/patologia , Carcinoma Adrenocortical/patologia , Neoplasias das Glândulas Suprarrenais/diagnóstico por imagem , Neoplasias das Glândulas Suprarrenais/cirurgia , Neoplasias das Glândulas Suprarrenais/ultraestrutura , Adrenalectomia/métodos , Carcinoma Adrenocortical/diagnóstico por imagem , Carcinoma Adrenocortical/cirurgia , Carcinoma Adrenocortical/ultraestrutura , Feminino , Humanos , Laparotomia/métodos , Pessoa de Meia-Idade , Estadiamento de Neoplasias , Tomografia Computadorizada por Raios X/métodos , Ultrassonografia/métodosRESUMO
Published reports of benign nerve sheath tumors of the larynx are extremely rare. Because these tumors represent a potential threat to the airway, prompt diagnosis and treatment are vital. We report a case of a neurilemmoma that arose from the right arytenoid muscle adjacent to the arytenoid cartilage. The mass was completely excised, and no recurrence was observed during follow-up. We discuss the diagnosis and management of this rare tumor.
