RESUMO
Near-infrared spectroscopy was used to monitor cerebral and mesenteric regional oximetry in a preterm neonate undergoing surgical ligation of a patent ductus arteriosus. This patient initially demonstrated severe mesenteric oxyhemoglobin desaturation, which improved immediately following ductal ligation.
Assuntos
Apneia/fisiopatologia , Permeabilidade do Canal Arterial/cirurgia , Oxiemoglobinas/metabolismo , Cerebelo/irrigação sanguínea , Permeabilidade do Canal Arterial/diagnóstico por imagem , Ecocardiografia , Embolização Terapêutica , Feminino , Humanos , Recém-Nascido , Recém-Nascido Prematuro , Mesentério/irrigação sanguínea , Monitorização Intraoperatória , Oximetria , Espectroscopia de Luz Próxima ao InfravermelhoRESUMO
In recent years, left ventricular noncompaction (LVNC) has been recognized as a distinct form of cardiomyopathy with its own clinical presentation and natural history. More than 100 cases of LVNC have been described in children. Although LVNC has been described in association with metabolic disorders such as Fabry's disease or genetic disorders such as Roifman's syndrome, this case represents the first report of LVNC in a child with trisomy 13.