RESUMO
Scimitar syndrome is a rare congenital abnormality. Clear anatomic definition is an important issue before operation. We report definition of both abnormal pulmonary venous drainage and anomalous systemic arterial supply by gadolinium-enhanced magnetic resonance angiography and three-dimensional computerized tomography in an eight month-old infant with scimitar syndrome. The presented case study confirms that these noninvasive diagnostic tools can successfully be used to provide valuable information about vascular anatomy in infants with scimitar syndrome.
Assuntos
Angiografia por Ressonância Magnética , Síndrome de Cimitarra/diagnóstico , Tomografia Computadorizada por Raios X/métodos , Dispneia/etiologia , Insuficiência de Crescimento/etiologia , Feminino , Humanos , Imageamento Tridimensional , Lactente , Síndrome de Cimitarra/complicações , Veias/patologiaRESUMO
Acute pulmonary hypertensive crisis is a fatal complication after obstructive TAPVC repair. An atrial septectomy or enlargement of a small ASD could be a lifesaving procedure in order to maintain cardiac output in severe cases. This procedure can be accomplished with inflow occlusion in patients with critical condition.
Assuntos
Cardiopatias Congênitas/cirurgia , Comunicação Interatrial/cirurgia , Hipertensão Pulmonar/etiologia , Veias Pulmonares/anormalidades , Doença Aguda , Evolução Fatal , Feminino , Humanos , LactenteRESUMO
Prolonged pleural effusions following a Fontan operation are a difficult problem. Although fenestrations and embolizations of systemic-pulmonary artery collaterals were suggested to treat and to decrease the risk of this complication, talc slurry pleurodesis may successfully augment and accelerate the beneficial effects of those techniques against the resistant effusions.
