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Arch Mal Coeur Vaiss ; 96(6): 677-82, 2003 Jun.
Artigo em Francês | MEDLINE | ID: mdl-12868351

RESUMO

Cardiac sarcoidosis is often unrecognised because of the absence of specific clinical and electrical signs. The consequences are serious, the main risk being sudden death due to conduction defects (24 to 31% of cases) or ventricular arrhythmias. Any conduction defect without an obvious cause in a young patient should suggest a possible diagnosis of sarcoidosis. The confirmation is histological when giant cell non-caseuting epithelioid granuloma is demonstrated but myocardial biopsies are only positive in 20% of cases. Therefore, biopsy of accessible organs such as salivary glands is recommended. Diagnostic strategy consists in searching for signs of systemic sarcoidosis, and, when the diagnosis has been established, perform a complete work-up with echocardiography, dipyridamole myocardial scintigraphy, cardiac MRI and 24 hour ambulatory ECG recordings (Holter). The only proven treatment is steroid therapy with occasional spectacular observations of reversibility of arrhythmias or conduction defects.


Assuntos
Corticosteroides/uso terapêutico , Cardiomiopatias/diagnóstico , Bloqueio Cardíaco/etiologia , Sarcoidose/diagnóstico , Adulto , Cardiomiopatias/tratamento farmacológico , Cardiomiopatias/fisiopatologia , Diagnóstico Diferencial , Ecocardiografia , Eletrocardiografia , Eletrocardiografia Ambulatorial , Feminino , Bloqueio Cardíaco/tratamento farmacológico , Bloqueio Cardíaco/fisiopatologia , Humanos , Imageamento por Ressonância Magnética , Sarcoidose/tratamento farmacológico , Sarcoidose/fisiopatologia , Resultado do Tratamento
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