[Leukoencephalitis with hemiplegia during chickenpox]. / Leucoencéphalite avec hémiplégie au cours d'une varicelle.

BACKGROUND: Chickenpox encephalitis is usually mild and often presents as an acute cerebellar ataxia. Seizures and coma are uncommon. CASE REPORT: A 4-year old girl presented generalized seizures. Two days after the onset of chickenpox, she developed ataxia and left hemiparesis on day 3, followed by left hemiplegia after 24 hours. The cerebral scan showed areas of subcortical hypodensity compatible with leuko-encephalitis. The EEG showed lesions of acute leuko-encephalitis located in the right sub-cortical temporo-fronto-parietal area. The patient was given cortico-steroid and recovered slowly but completely. CONCLUSIONS: Hemiplegia, an exceptional event during the course of chickenpox, makes the diagnosis of chickenpox leuko-encephalitis difficult; IRM appears to be a contributing factor.

[Problems posed by the association of hemophilia A and congenital adrenal hyperplasia caused by 21-hydroxylase deficiency]. / Problèmes posés par l'association hémophilie A et hyperplasie congénitale des surrenales par déficit en 21 hydroxylase.

Association of congenital adrenal hyperplasia (21 hydroxylase deficiency) and hemophilia A in one child is reported; the authors insist about the rarity and the genetic implications of this association in case of other children.